Evaluation of 10-Year Experience of Wegener's Granulomatosis in Iranian Children.
Wegener's granulomatosis or granulomatosis polyangiitis (GPA) is an uncommon chronic systemic vasculitis in children. The aim of this study was to describe pediatric patients with GPA in Iran. We studied records of all patients with GPA diagnosis who were referred to all Iranian Pediatric Rheumatolo...
| Publicado en: | ISRN Rheumatology pp. 1 - 5 |
|---|---|
| Autores principales: | , , , , , , , |
| Formato: | research tables/charts Journal Article |
| Publicado: |
Wiley-Blackwell
2013
|
| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=104048966&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 104048966 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 20905467 BFDP jtl: ISRN Rheumatology issn: 20905467 maglogo: N pubinfo: dt: 2013 pid: 480 pub: Wiley-Blackwell place: Malden, Massachusetts artinfo: ui: 104048966 104048966 2012510475 104048966 ppf: 1 ppct: 4 formats: fmt: @attributes: type: P tig: atl: Evaluation of 10-Year Experience of Wegener's Granulomatosis in Iranian Children. aug: au: Tahghighi, Fatemeh Moradinejad, Mohamad-Hassan Aghighi, Yahya Shiari, Reza Raeeskarami, Seyed-Reza Salehzadeh, Farhad Javadi, Vadood Ziaee, Vahid affil: Pediatric Rheumatology Research Group, Rheumatology Research Center, Tehran University of Medical Sciences, Tehran, Iran sug: subj: Granulomatosis with Polyangiitis Epidemiology Symptoms Human Child Iran Retrospective Design Utilization Medical Records Utilization Male Female Hematologic Tests Utilization Child: 6-12 years Male Female ab: Wegener's granulomatosis or granulomatosis polyangiitis (GPA) is an uncommon chronic systemic vasculitis in children. The aim of this study was to describe pediatric patients with GPA in Iran. We studied records of all patients with GPA diagnosis who were referred to all Iranian Pediatric Rheumatology Division from 2002 to 2011. A total of 11 patients (5 females and 6 males) enrolled in this study. In children less than 15 years old, the prevalence of GPA is 0.6 per million. The mean age of GPA diagnosis was 11 years and average delay diagnosis was 20 months. Mortality rate was 18.1% due to pulmonary vasculitis and infection. The most common organ system involvement was upper and lower respiratory tract involvement (81.8% and 63.9%, resp.). Other common manifestations were renal (36.3), skin (27.2%), and eye involvement (18.2%). pubtype: Academic Journal doctype: research tables/charts Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
|---|