Primary immunodeficiency diseases at reference and high-specialty hospitals in the state of guanajuato, Mexico.

Background. In general, primary immunodeficiency diseases (PIDs) are underdiagnosed in most countries. The objective of this study was to describe the frequency and clinical spectrum of PID in the most important tertiary hospitals in our region. Methods. An observational, cross-sectional, with retro...

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Publicado en:BioMed Research International Vol. 2013; pp. 187254 - 187255
Autores principales: Guaní-Guerra, Eduardo, García-Ramírez, Ulises Noel, Jiménez-Romero, Ana Isabel, Velázquez-Avalos, José Manuel, Gallardo-Martínez, Gabriela, Mendoza-Espinoza, Francisco-Javier
Formato: research Journal Article
Publicado: Wiley-Blackwell 2013
Acceso en línea:Ver este registro en EBSCOhost
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      dt: 2013
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      pub: Wiley-Blackwell
      place: Malden, Massachusetts
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        atl: Primary immunodeficiency diseases at reference and high-specialty hospitals in the state of guanajuato, Mexico.
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          Guaní-Guerra, Eduardo
          García-Ramírez, Ulises Noel
          Jiménez-Romero, Ana Isabel
          Velázquez-Avalos, José Manuel
          Gallardo-Martínez, Gabriela
          Mendoza-Espinoza, Francisco-Javier
        affil: Departamento de Inmunología, Hospital Regional de Alta Especialidad del Bajío, Boulevard Milenio 130 San Carlos La Roncha, 37660 León, GTO, Mexico.
      sug:
        subj:
          Hospitals Statistics and Numerical Data
          Immunologic Deficiency Syndromes Epidemiology
          Adolescence
          Child
          Female
          Human
          Immunologic Deficiency Syndromes Etiology
          Immunologic Deficiency Syndromes Pathology
          Male
          Mexico
          Adolescent: 13-18 years
          Child: 6-12 years
          Female
          Male
      ab: Background. In general, primary immunodeficiency diseases (PIDs) are underdiagnosed in most countries. The objective of this study was to describe the frequency and clinical spectrum of PID in the most important tertiary hospitals in our region. Methods. An observational, cross-sectional, with retrospective chart, review study was conducted. A total of 26 patients were included and grouped according to the updated classification of PIDs. Results. PIDs spectra were as follows: predominantly antibody deficiency diseases were the most common category (65.38%), followed by other well-defined immunodeficiency syndromes (11.55%), congenital defects of phagocyte number and/or function (7.69%), complement deficiencies (3.85%), combined T- and B-cell immunodeficiencies (3.85%), and defects in innate immunity (3.85%). The mean time elapsed from the onset of symptoms to the reference and diagnosis by a tertiary hospital was of 4.65 ± 6.95 years. Conclusions. Predominant antibody deficiency disease was the most common group of PIDs, agreeing with international reports. Awareness of underdiagnosis by physicians is crucial for a prompt diagnosis and treatment, which in turn should improve the quality of life among patients with PIDs.
      pubtype: Academic Journal
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        Journal Article
      ougenre: Article
    language: English
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