Pseudoxanthoma elasticum with mallory-weiss syndrome: case report.

Pseudoxanthoma elasticum is a multi-systemic, genetic disorder of the connective tissue characterized by progressive calcification and fragmentation of elastic fibers in skin, retina, gastrointestinal and cardiovascular systems. Skin changes generally manifest in adulthood and rarely in childhood. U...

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Published in:Turkiye Klinikleri Journal of Medical Sciences Vol. 32; no. 3; pp. 887 - 891
Main Authors: Türköz, Fatma Paksoy, Ulas, Turgay, Bes, Cemal, Özkan, Koray, Sakiz, Damlanur, Sinan, Mehmet, Borlu, Fatih
Format: case study pictorial Journal Article
Published: Turkiye Klinikleri Jun2012
Online Access:View this record in EBSCOhost
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      dt: Jun2012
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      pub: Turkiye Klinikleri
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        atl: Pseudoxanthoma elasticum with mallory-weiss syndrome: case report.
      aug:
        au:
          Türköz, Fatma Paksoy
          Ulas, Turgay
          Bes, Cemal
          Özkan, Koray
          Sakiz, Damlanur
          Sinan, Mehmet
          Borlu, Fatih
      sug:
        subj:
          Esophageal Perforation
          Vascular Diseases
          Female
          Middle Age
          Middle Aged: 45-64 years
          Female
      ab: Pseudoxanthoma elasticum is a multi-systemic, genetic disorder of the connective tissue characterized by progressive calcification and fragmentation of elastic fibers in skin, retina, gastrointestinal and cardiovascular systems. Skin changes generally manifest in adulthood and rarely in childhood. Upper gastrointestinal hemorrhage occurs in some cases and is frequently resistant to nonsurgical methods of treatment. As the prognosis of pseudoxanthoma elasticum is related to the involvement of extracutaneous organs, early recognition of the disease is important to take preventive measures and to decrease the morbidity. Herein, we presented a case of pseudoxanthoma elasticum with Mallory-Weiss syndrome, who had repetitive and massive upper gastrointestinal bleeding. To our knowledge, there is no reported case of pseudoxanthoma elasticum with Mallory-Weiss syndrome in the literature.
      pubtype: Academic Journal
      doctype:
        case study
        pictorial
        Journal Article
      ougenre: Article
    language: Turkish
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