Diffusion-Weighted Magnetic Resonance Imaging and Proton Magnetic Resonance Spectroscopy of Sjögren-Larsson Syndrome: Case Report.

Sjögren-Larsson syndrome (SLS) is a rare, autosomal recessive congenital disorder that affects mainly skin and central nervous system. It is characterized by spastic diplegia or tetraplegia, mental retardation and congenital ichthyosis. We report a 2-year-old patient with SLS in whom both mildly res...

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Publicado en:Turkiye Klinikleri Journal of Medical Sciences Vol. 31; no. 6; pp. 1578 - 1585
Autores principales: Karadeli, Elif, Ulu, E. Meltem Kayahan, Teksam, Mehmet
Formato: case study diagnostic images tracings Journal Article
Publicado: Turkiye Klinikleri Nov/Dec2011
Acceso en línea:Ver este registro en EBSCOhost