Difficulty diagnosing chronic cryptococcal meningitis in idiopathic CD4+ lymphocytopenia.

A 64-year-old man with idiopathic CD4(+) lymphocytopenia developed cognitive impairment and gait ataxia with isolated obstructive hydrocephalus, which was fatal. Cerebrospinal fluid showed mild pleocytosis, but the etiology was not revealed by extensive analysis. At autopsy, inflammatory cells, CD8(...

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Publicado en:Neurological Sciences Vol. 32; no. 3; pp. 519 - 525
Autores principales: Sancesario G, Palmieri G, Viola G, Fontana C, Perfetti A, Anemona L, Floris R, Marziali S, Bernardi G, Spagnoli LG, Sancesario, Giuseppe, Palmieri, Giampiero, Viola, Gemma, Fontana, Carla, Perfetti, Alessandra, Anemona, Lucia, Floris, Roberto, Marziali, Simone, Bernardi, Giorgio, Spagnoli, Luigi Giusto
Formato: case study Journal Article
Publicado: Springer Nature Jun2011
Acceso en línea:Ver este registro en EBSCOhost
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      dt: Jun2011
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      pub: Springer Nature
      place: New York, New York
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        10.1007/s10072-011-0496-5
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        atl: Difficulty diagnosing chronic cryptococcal meningitis in idiopathic CD4+ lymphocytopenia.
      aug:
        au:
          Sancesario G
          Palmieri G
          Viola G
          Fontana C
          Perfetti A
          Anemona L
          Floris R
          Marziali S
          Bernardi G
          Spagnoli LG
          Sancesario, Giuseppe
          Palmieri, Giampiero
          Viola, Gemma
          Fontana, Carla
          Perfetti, Alessandra
          Anemona, Lucia
          Floris, Roberto
          Marziali, Simone
          Bernardi, Giorgio
          Spagnoli, Luigi Giusto
        affil: Dipartimento di Neuroscienze, Università di Roma Tor Vergata, Via Montpellier 1, 00133 Rome, Italy
      sug:
        subj:
          Cryptococcus
          Hydrocephalus Complications
          Hydrocephalus Microbiology
          Meningitis, Cryptococcal Complications
          Lymphopenia Complications
          Chronic Disease
          Diagnosis, Differential
          Fatal Outcome
          Hydrocephalus Diagnosis
          Male
          Meningitis, Cryptococcal Diagnosis
          Meningitis, Cryptococcal Microbiology
          Middle Age
          Lymphopenia Diagnosis
          Lymphopenia Microbiology
          Middle Aged: 45-64 years
          Male
      ab: A 64-year-old man with idiopathic CD4(+) lymphocytopenia developed cognitive impairment and gait ataxia with isolated obstructive hydrocephalus, which was fatal. Cerebrospinal fluid showed mild pleocytosis, but the etiology was not revealed by extensive analysis. At autopsy, inflammatory cells, CD8(+) lymphocytes and abundant macrophages but not CD4(+) lymphocytes were infiltrating the meninges at the base of the brain. Electron microscopy demonstrated that inflammation was caused by Cryptococcus neoformans, which was localized exclusively within macrophages, where it grew with budding. Our study suggests that, in idiopathic CD4(+) lymphocytopenia, macrophages can efficiently phagocytize but inefficiently digest C. neoformans, thus representing a vehicle of chronic intracellular infection.
      pubtype: Academic Journal
      doctype:
        case study
        Journal Article
      ougenre: Article
    language: English
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