Autoinflammatory pustular neutrophilic diseases.

This article provides a new categorization of inflammatory pustular dermatoses in the context of recent genetic and biological insights. Monogenic diseases with pustular phenotypes are discussed, including deficiency of interleukin 1 receptor antagonist, deficiency of the interleukin 36 receptor ant...

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Publicado en:Dermatologic Clinics Vol. 31; no. 3; pp. 405 - 426
Autores principales: Naik, Haley B, Cowen, Edward W
Formato: Journal Article
Publicado: W B Saunders 2013 Jul
Acceso en línea:Ver este registro en EBSCOhost
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      dt: 2013 Jul
      vid: 31
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      pub: W B Saunders
      place: Philadelphia, Pennsylvania
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        10.1016/j.det.2013.04.001
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        atl: Autoinflammatory pustular neutrophilic diseases.
      aug:
        au:
          Naik, Haley B
          Cowen, Edward W
        affil: Dermatology Branch, Center for Cancer Research, National Cancer Institute, National Institutes of Health, Building 10, Room 12N238, 10 Center Drive, MSC 1908, Bethesda, MD 20892-1908, USA.
      sug:
        subj:
          Autoimmune Diseases Diagnosis
          Neutrophils Immunology
          Skin Diseases, Vesiculobullous Diagnosis
          Autoimmune Diseases Drug Therapy
          Autoimmune Diseases Immunology
          Diagnosis, Differential
          Skin Diseases, Vesiculobullous Drug Therapy
          Skin Diseases, Vesiculobullous Immunology
      ab: This article provides a new categorization of inflammatory pustular dermatoses in the context of recent genetic and biological insights. Monogenic diseases with pustular phenotypes are discussed, including deficiency of interleukin 1 receptor antagonist, deficiency of the interleukin 36 receptor antagonist, CARD14-associated pustular psoriasis, and pyogenic arthritis, pyoderma gangrenosum, and acne. How these new genetic advancements may inform how previously described pustular diseases are viewed, including pustular psoriasis and its clinical variants, with a focus on historical classification by clinical phenotype, is also discussed.
      pubtype: Academic Journal
      doctype: Journal Article
      ougenre: Article
    language: English
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