Autoinflammatory diseases in pediatrics.
Autoinflammatory diseases (AIDs) are characterized by recurrent episodes of systemic and organ-specific inflammation. Many of these diseases share fever as a common presenting feature. Physicians need to consider AIDs in children with recurrent, unexplained fevers, when infectious and malignant caus...
| Publicado en: | Dermatologic Clinics Vol. 31; no. 3; pp. 481 - 495 |
|---|---|
| Autores principales: | , |
| Formato: | Journal Article |
| Publicado: |
W B Saunders
2013 Jul
|
| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=107907294&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 107907294 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 07338635 DO3 jtl: Dermatologic Clinics issn: 07338635 maglogo: N pubinfo: dt: 2013 Jul vid: 31 iid: 3 pid: 1351 pub: W B Saunders place: Philadelphia, Pennsylvania artinfo: ui: 107907294 2012177751 10.1016/j.det.2013.04.003 NLM23827250 107907294 ppf: 481 ppct: 14 formats: tig: atl: Autoinflammatory diseases in pediatrics. aug: au: Hausmann, Jonathan S Dedeoglu, Fatma affil: Program in Rheumatology, Division of Immunology, Boston Children's Hospital, 300 Longwood Avenue, Boston, MA 02115, USA. Electronic address: jonathan.hausmann@childrens.harvard.edu. sug: subj: Autoimmune Diseases Complications Hereditary Autoinflammatory Diseases Complications Antiinflammatory Agents Therapeutic Use Analgesics, Nonnarcotic Therapeutic Use Autoimmune Diseases Diagnosis Autoimmune Diseases Drug Therapy Child Child, Preschool Diagnosis, Differential Fever Drug Therapy Fever Etiology Hereditary Autoinflammatory Diseases Diagnosis Hereditary Autoinflammatory Diseases Drug Therapy Infant Inflammation Drug Therapy Inflammation Etiology Syndrome Child: 6-12 years Child, Preschool: 2-5 years Infant: 1-23 months ab: Autoinflammatory diseases (AIDs) are characterized by recurrent episodes of systemic and organ-specific inflammation. Many of these diseases share fever as a common presenting feature. Physicians need to consider AIDs in children with recurrent, unexplained fevers, when infectious and malignant causes have been discarded. This article discusses the differential diagnosis of recurrent fever in children, with a focus on AIDs. It discusses pharyngitis, and cervical adenitis and the monogenic autoinflammatory diseases that cause recurrent fevers including familial Mediterranean fever, hyper-immunoglobulin (Ig) D and periodic fever syndrome, tumor necrosis factor receptor-associated periodic syndrome, cryopyrin associated periodic syndromes, deficiency of interleukin-36 receptor antagonist, Majeed syndrome, chronic atypical neutrophilic dermatosis with lipodystrophy and increased temperature syndrome, and deficiency of the interleukin-1 receptor antagonist. In addition, the granulomatous disorders, pyogenic sterile arthritis, pyoderma gangrenosum, and acne and Blau syndrome, will be discussed. pubtype: Academic Journal doctype: Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
|---|