Pyoderma Vegetans: A Case Report in a Child Suspected to Primary Immunodeiciency and Review of the Literature.
Pyoderma vegetans (PV) is a rare inflammatory disorder characterized by vegetating pustules and plaques affecting the skin and mucosal membranes. It is believed that this entity is mostly associated with inflammatory bowel disease (IBD), chronic malnutrition, human immunodeficiency virus (HIV), mali...
| Publicado en: | Iranian Journal of Medical Sciences Vol. 40; no. 4; pp. 381 - 386 |
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| Autores principales: | , , , , |
| Formato: | case study pictorial Journal Article |
| Publicado: |
Shiraz University of Medical Sciences
Jul2015
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| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=108402515&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 108402515 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 02530716 8TQH jtl: Iranian Journal of Medical Sciences issn: 02530716 maglogo: N pubinfo: dt: Jul2015 vid: 40 iid: 4 pid: 65846 pub: Shiraz University of Medical Sciences place: Shiraz, <Blank> artinfo: ui: 108402515 108402515 109832785 108402515 ppf: 381 ppct: 5 formats: tig: atl: Pyoderma Vegetans: A Case Report in a Child Suspected to Primary Immunodeiciency and Review of the Literature. aug: au: Mansouri, Mahboubeh Rakhshan, Azadeh Shahidi-Dadras, Mohammad Karimi, Abdollah Alavi, Samin affil: Department of Immunology and Allergy, Mofid Children Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran sug: subj: Pyoderma Severe Combined Immunodeficiency Complications Child Female Child: 6-12 years Female ab: Pyoderma vegetans (PV) is a rare inflammatory disorder characterized by vegetating pustules and plaques affecting the skin and mucosal membranes. It is believed that this entity is mostly associated with inflammatory bowel disease (IBD), chronic malnutrition, human immunodeficiency virus (HIV), malignancies, and other immunocompromised states. Pyoderma vegetans occurs more commonly in young and middle-aged adults. There is no sex predilection for this entity. The lesions could heal spontaneously, but usually recur and become chronic. Our patient was an 11-year-old girl suspected to have primary combined immunodeficiency complicated by chronic recurrent vegetating pustular lesions on the face and postauricular area since one year of age. The histological features of the lesions were consistent with pyoderma vegetans. This is the first case of PV beginning from early infancy in the setting of primary immunodeficiency and in an unusual location. pubtype: Academic Journal doctype: case study pictorial Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
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