Corpus Callosum Diffusion and Connectivity Features in High Functioning Subjects With Pyridoxine-Dependent Epilepsy.

Background: In this observational study, white matter structure, functional magnetic resonance imaging (fMRI) task-based responses, and functional connectivity were assessed in four subjects with high functioning pyridoxine-dependent epilepsy and age-matched control subjects.Methods: Four male subje...

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Publicado en:Pediatric Neurology Vol. 54; pp. 43 - 49
Autores principales: Poliachik, Sandra L., Friedman, Seth D., Poliakov, Andrew V., Budech, Christopher B., Ishak, Gisele E., Shaw, Dennis W.W., Jr.,Gospe, Sidney M., Gospe, Sidney M Jr
Formato: research Journal Article
Publicado: Elsevier B.V. Jan2016
Acceso en línea:Ver este registro en EBSCOhost
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      dt: Jan2016
      vid: 54
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      pub: Elsevier B.V.
      place: New York, New York
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        atl: Corpus Callosum Diffusion and Connectivity Features in High Functioning Subjects With Pyridoxine-Dependent Epilepsy.
      aug:
        au:
          Poliachik, Sandra L.
          Friedman, Seth D.
          Poliakov, Andrew V.
          Budech, Christopher B.
          Ishak, Gisele E.
          Shaw, Dennis W.W.
          Jr.,Gospe, Sidney M.
          Gospe, Sidney M Jr
        affil: Department of Radiology, Seattle Children's Hospital, Seattle Washington
      sug:
        subj:
          Telencephalon Pathology
          Epilepsy Pathology
          Epilepsy Physiopathology
          Telencephalon Physiopathology
          Middle Age
          Magnetic Resonance Imaging
          Relaxation
          Neural Pathways Pathology
          Adult
          Brain Physiopathology
          Neural Pathways Physiopathology
          Brain Pathology
          Severity of Illness Indices
          Young Adult
          Male
          Mental Processes
          Neuropsychological Tests
          Human
          Middle Aged: 45-64 years
          Adult: 19-44 years
          Male
      ab: Background: In this observational study, white matter structure, functional magnetic resonance imaging (fMRI) task-based responses, and functional connectivity were assessed in four subjects with high functioning pyridoxine-dependent epilepsy and age-matched control subjects.Methods: Four male subjects with pyridoxine-dependent epilepsy (mean age 31 years 8 months, standard deviation 12 years 3 months) and age-matched control subjects (32 years 4 months, standard deviation 13 years) were recruited to participate in the study. Diffusion tensor data were collected and postprocessed in Functional Magnetic Resonance Imaging of the Brain Software Library to quantify corpus callosum tracts as a means to assess white matter structure. Task-based fMRI data were collected and Functional Magnetic Resonance Imaging of the Brain Software Library used to assess task response. The fMRI resting-state data were analyzed with the functional connectivity toolbox Conn to determine functional connectivity.Results: Subjects with high functioning pyridoxine-dependent epilepsy retained structural white matter connectivity compared with control subjects, despite morphologic differences in the posterior corpus callosum. fMRI task-based results did not differ between subjects with pyridoxine-dependent epilepsy and control subjects; functional connectivity as measured with resting-state fMRI was lower in subjects with pyridoxine-dependent epilepsy for several systems (memory, somatosensory, auditory).Conclusion: Although corpus callosum morphology is diminished in the posterior portions, structural connectivity was retained in subjects with pyridoxine-dependent epilepsy, while functional connectivity was diminished for memory, somatosensory, and auditory systems.
      pubtype: Academic Journal
      doctype:
        research
        Journal Article
      ougenre: Article
    language: English
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