Clinical Findings and Management of Septo-Optic Dysplasia.

Background: Septo-optic dysplasia is a congenital condition involving optic nerve hypoplasia, an absent septum pellucidum, and thinning of the corpus callosum. Endocrine dysfunctions may also be present. While only 30% of patients have a triad of optic nerve hypoplasia, absence of the septum pelluci...

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Publicado en:Optometry & Visual Performance Vol. 4; no. 2; pp. 72 - 77
Autor principal: Tison, Kara
Formato: case study diagnostic images tables/charts Journal Article
Publicado: Optometric Extension Program May2016
Acceso en línea:Ver este registro en EBSCOhost
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      dt: May2016
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      pub: Optometric Extension Program
      place: Lutherville Timonium, Maryland
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        atl: Clinical Findings and Management of Septo-Optic Dysplasia.
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        au: Tison, Kara
        affil: OD, University of the Incarnate Word, Rosenberg School of Optometry, San Antonio, Texas
      sug:
        subj:
          Optic Nerve
          Pupil Disorders
          Magnetic Resonance Imaging
          Tomography, Optical Coherence
          Vision Screening
          Male
          Male
      ab: Background: Septo-optic dysplasia is a congenital condition involving optic nerve hypoplasia, an absent septum pellucidum, and thinning of the corpus callosum. Endocrine dysfunctions may also be present. While only 30% of patients have a triad of optic nerve hypoplasia, absence of the septum pellucidum, and pituitary dysfunctions, early diagnosis of this disorder is important. Case Report: A six-year-old male presented with a history of failing a school vision screening. The entering acuities, and subsequently the best-corrected visual acuities, were 20/500 OD, 20/20 OS. An afferent pupillary defect was present OD. Cup-to-disc ratios were 0.45H/0.50V OD, 0.30H/0.35V OS. Optical coherence tomography confirmed OD to be smaller in size than OS. Magnetic Resonance Imaging (MRI) revealed a hypoplastic optic nerve OD and partial absence of the septum pellucidum, consistent with the diagnosis of septo-optic dysplasia. Conclusion: This case outlines the presentation of the patient, diagnostic testing, appropriate referrals, and management available for patients with septo-optic dysplasia.
      pubtype: Academic Journal
      doctype:
        case study
        diagnostic images
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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