Cerebral vascular findings in PAPA syndrome: cerebral arterial vasculopathy or vasculitis and a posterior cerebral artery dissecting aneurysm.

A young patient with PAPA (pyogenic arthritis, pyoderma gangrenosum, and acne) syndrome developed an unusual cerebral arterial vasculopathy/vasculitis (CAV) that resulted in subarachnoid hemorrhage from a ruptured dissecting posterior cerebral artery (PCA) aneurysm. This aneurysm was successfully tr...

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Bibliographic Details
Published in:	Journal of NeuroInterventional Surgery Vol. 8; no. 8; pp. 615 - 619
Main Authors:	Khatibi, Kasra, Heit, Jeremy J., Telischak, Nicholas A., Elbers, Jorina M., Do, Huy M.
Format:	case study diagnostic images Journal Article
Published:	BMJ Publishing Group Aug2016
Online Access:	View this record in EBSCOhost

Description
Summary:	A young patient with PAPA (pyogenic arthritis, pyoderma gangrenosum, and acne) syndrome developed an unusual cerebral arterial vasculopathy/vasculitis (CAV) that resulted in subarachnoid hemorrhage from a ruptured dissecting posterior cerebral artery (PCA) aneurysm. This aneurysm was successfully treated by endovascular coil sacrifice of the affected segment of the PCA. The patient made an excellent recovery with no significant residual neurologic deficit.