Alarming consequences - autoinflammatory disease spectrum due to mutations in proline-serine-threonine phosphatase-interacting protein 1.

Purpose Of Review: To give an overview about the expanding spectrum of autoinflammatory diseases due to mutations in proline-serine-threonine phosphatase-interacting protein 1 (PSTPIP1) and new insights into their pathogenesis.Recent Findings: In addition to classical pyogenic sterile arthritis, pyo...

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Publicado en:Current Opinion in Rheumatology Vol. 28; no. 5; pp. 550 - 560
Autores principales: Holzinger, Dirk, Roth, Johannes
Formato: review Journal Article
Publicado: Lippincott Williams & Wilkins Sep2016
Acceso en línea:Ver este registro en EBSCOhost