Saddle-nose and bilateral cauliflower ear deformities with pyoderma gangrenosum-like ulcers, cavitary pulmonary lesions, digital gangrene and pulselessness in a young female.

We report a young female who presented with saddlenose and bilateral cauliflower ear deformities along with pyoderma gangrenosum-like ulcers, digital gangrene and pulselessness. Subsequently, she was found to have bilateral conductive hearing loss, a corneal opacity, mild aortic regurgitation and ra...

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Publicado en:BMJ Case Reports Vol. 2017; pp. 1 - 5
Autores principales: Subhadarshani, Sweta, Gupta, Vishal, Chahal, Anurag, Verma, Kaushal K.
Formato: Journal Article
Publicado: BMJ Publishing Group 6/15/2017
Acceso en línea:Ver este registro en EBSCOhost
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        10.1136/bcr-2017-220434
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        atl: Saddle-nose and bilateral cauliflower ear deformities with pyoderma gangrenosum-like ulcers, cavitary pulmonary lesions, digital gangrene and pulselessness in a young female.
      aug:
        au:
          Subhadarshani, Sweta
          Gupta, Vishal
          Chahal, Anurag
          Verma, Kaushal K.
        affil: Department of Dermatology and Venereology, All India Institute of Medical Sciences, New Delhi, Delhi, India
      sug:
      ab: We report a young female who presented with saddlenose and bilateral cauliflower ear deformities along with pyoderma gangrenosum-like ulcers, digital gangrene and pulselessness. Subsequently, she was found to have bilateral conductive hearing loss, a corneal opacity, mild aortic regurgitation and radiological evidence of cavitary changes in lungs and aortoarteritis. Our patient had a constellation of symptoms which posed a diagnostic challenge. Finally, a diagnosis of relapsing polychondritis with several unusual features was made. Overlap with Takayasu's arteritis and granulomatosis with polyangitis, which has been reported rarely in the literature, cannot be excluded.
      pubtype: Academic Journal
      doctype: Journal Article
      ougenre: Article
    language: English
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