Erythema elevatum diutinum in Crohn's disease-associated spondyloarthritis - a rare vasculitis, an unusual association.
Erythema elevatum diutinum is a rare neutrophilic dermatosis with vasculitis, which presents as persistent, symmetrical, purple or brownish papules and nodules, mainly in the extensor surface of the limbs. We describe a case of erythema elevatum diutinum and polyarthritis as initial manifestations o...
| Published in: | Acta Reumatológica Portuguesa no. 4; pp. 324 - 329 |
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| Main Authors: | , , , , , , |
| Format: | Article |
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Sociedade Portuguesa de Reumatologia
oct-dez2017
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| Subjects: | |
| Online Access: | View this record in EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=lth&AN=127155811&site=ehost-live header: @attributes: shortDbName: lth uiTerm: 127155811 longDbName: MedicLatina uiTag: AN controlInfo: bkinfo: jinfo: jid: 0303464X 4Z1D jtl: Acta Reumatológica Portuguesa issn: 0303464X maglogo: N pubinfo: dt: oct-dez2017 iid: 4 pid: 38819 pub: Sociedade Portuguesa de Reumatologia artinfo: ui: 127155811 ppf: 324 ppct: 5 formats: fmt: @attributes: type: P size: 513KB tig: atl: Erythema elevatum diutinum in Crohn's disease-associated spondyloarthritis - a rare vasculitis, an unusual association. aug: au: M. J., Gonçalves V. C., Romão L., Soares-de-Almeida H., Canhão J. C., Romeu H., Kutzner J. A., Pereira-da-Silva affil: Reumatologia, Centro Hospitalar Lisboa Norte; Unidade de Investigação em Reumatologia, Instituto de Medicina Molecular Dermatologia, Centro Hospitalar Lisboa Norte EpiDoC, CEDOC, Nova medical school Dermatopathologie Friedrichshafen, Friedrichshafen su: Crohn's disease Erythema Vasculitis Arthritis Tuberculosis treatment sug: subj: Crohn's disease Erythema Vasculitis Arthritis Tuberculosis treatment keyword: Crohn's disea - se Cutaneous vasculitis Erythema elevatum diutinum Spondyloarthritis ab: Erythema elevatum diutinum is a rare neutrophilic dermatosis with vasculitis, which presents as persistent, symmetrical, purple or brownish papules and nodules, mainly in the extensor surface of the limbs. We describe a case of erythema elevatum diutinum and polyarthritis as initial manifestations of Crohn's disea se associated spondyloarthritis. A 51-year-old man, from São Tomé e Príncipe, with previous history of treated tuberculosis and chronic hepatitis B infection, was admitted due to 4 months history of polyarthritis, hyperpigmented papules on the extensor surfaces, occasional episodes of bloody mucous diarrhea and significant weight loss. Histology of the skin showed myeloperoxidase positive neutrophilic granulocytes with moderate karyorrhexis, consistent with erythema elevatum diutinum. Colonoscopy showed erosions in sigmoid and rectum. Diagnosis of erythema elevatum diutinum secondary to Crohn's disease with associated peripheral spondyloarthritis was assumed. The patient was treated with prednisolone, sulphasalazine, metronidazole, azathioprine and tenofovir with good clinical response. As erythema elevatum diutinum can be secondary to multiple systemic diseases, including rheumatic diseases and inflammatory bowel disease, being aware and re - cognizing this entity can be of great importance for rheumatologists. pubtype: Academic Journal doctype: Article src: R language: English refInfo: copyright: @attributes: flag: Y custom: Copyright of Acta Reumatológica Portuguesa is the property of Sociedade Portuguesa de Reumatologia and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. item: Acta Reumatológica Portuguesa holder: Sociedade Portuguesa de Reumatologia dt: @attributes: year: 2017 holdings: @attributes: islocal: N |
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