Diagnostic Criteria of Ulcerative Pyoderma Gangrenosum: A Delphi Consensus of International Experts.

Importance: Pyoderma gangrenosum is a rare inflammatory skin condition that is difficult to diagnose. Currently, it is a "diagnosis of exclusion," a definition not compatible with clinical decision making or inclusion for clinical trials.Objective: To propose and validate diagnostic criteria for ulc...

Descripción completa

Detalles Bibliográficos
Publicado en:JAMA Dermatology Vol. 154; no. 4; pp. 461 - 467
Autores principales: Maverakis, Emanual, Ma, Chelsea, Shinkai, Kanade, Fiorentino, David, Callen, Jeffrey P., Wollina, Uwe, Marzano, Angelo Valerio, Wallach, Daniel, Kim, Kyoungmi, Schadt, Courtney, Ormerod, Anthony, Fung, Maxwell A., Steel, Andrea, Patel, Forum, Qin, Rosie, Craig, Fiona, Williams, Hywel C., Powell, Frank, Merleev, Alexander, Cheng, Michelle Y.
Formato: pictorial research tables/charts Journal Article
Publicado: American Medical Association Apr2018
Acceso en línea:Ver este registro en EBSCOhost
fields @attributes:
  recordID: 1
pdfLink:
plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=129044491&site=ehost-live
header:
  @attributes:
    shortDbName: ccm
    uiTerm: 129044491
    longDbName: CINAHL Complete
    uiTag: AN
  controlInfo:
    bkinfo:
    dissinfo:
    jinfo:
      jid:
        21686068
        FTFQ
      jtl: JAMA Dermatology
      issn: 21686068
      maglogo: N
    pubinfo:
      dt: Apr2018
      vid: 154
      iid: 4
      pid: 30
      pub: American Medical Association
      place: Chicago, Illinois
    artinfo:
      ui:
        129044491
        129044491
        NLM29450466
        129044491
        10.1001/jamadermatol.2017.5980
        NLM29450466
        129044491
      ppf: 461
      ppct: 6
      formats:
      tig:
        atl: Diagnostic Criteria of Ulcerative Pyoderma Gangrenosum: A Delphi Consensus of International Experts.
      aug:
        au:
          Maverakis, Emanual
          Ma, Chelsea
          Shinkai, Kanade
          Fiorentino, David
          Callen, Jeffrey P.
          Wollina, Uwe
          Marzano, Angelo Valerio
          Wallach, Daniel
          Kim, Kyoungmi
          Schadt, Courtney
          Ormerod, Anthony
          Fung, Maxwell A.
          Steel, Andrea
          Patel, Forum
          Qin, Rosie
          Craig, Fiona
          Williams, Hywel C.
          Powell, Frank
          Merleev, Alexander
          Cheng, Michelle Y.
        affil: Department of Dermatology, University of California, Davis, Sacramento
      sug:
        subj:
          Pyoderma Gangrenosum Diagnosis
          Skin Pathology
          Pyoderma Gangrenosum Pathology
          Skin Ulcer Diagnosis
          ROC Curve
          Delphi Technique
          Pyoderma Gangrenosum Complications
          Neutrophils Pathology
          Biopsy
          Skin Ulcer Etiology
          Human
          Consensus
          Pharmacokinetics
      ab: Importance: Pyoderma gangrenosum is a rare inflammatory skin condition that is difficult to diagnose. Currently, it is a "diagnosis of exclusion," a definition not compatible with clinical decision making or inclusion for clinical trials.Objective: To propose and validate diagnostic criteria for ulcerative pyoderma gangrenosum.Evidence Review: Diagnostic criteria were created following a Delphi consensus exercise using the RAND/UCLA Appropriateness Method. The criteria were validated against peer-reviewed established cases of pyoderma gangrenosum and mimickers using k-fold cross-validation with methods of multiple imputation.Findings: Delphi exercise yielded 1 major criterion-biopsy of ulcer edge demonstrating neutrophilic infiltrate-and 8 minor criteria: (1) exclusion of infection; (2) pathergy; (3) history of inflammatory bowel disease or inflammatory arthritis; (4) history of papule, pustule, or vesicle ulcerating within 4 days of appearing; (5) peripheral erythema, undermining border, and tenderness at ulceration site; (6) multiple ulcerations, at least 1 on an anterior lower leg; (7) cribriform or "wrinkled paper" scar(s) at healed ulcer sites; and (8) decreased ulcer size within 1 month of initiating immunosuppressive medication(s). Receiver operating characteristic analysis revealed that 4 of 8 minor criteria maximized discrimination, yielding sensitivity and specificity of 86% and 90%, respectively.Conclusions and Relevance: This Delphi exercise produced 1 major criterion and 8 minor criteria for the diagnosis of ulcerative pyoderma gangrenosum. The criteria may serve as a guideline for clinicians, allowing for fewer misdiagnoses and improved patient selection for clinical trials.
      pubtype: Academic Journal
      doctype:
        pictorial
        research
        tables/charts
        Journal Article
      ougenre: Article
    language: English
    refInfo:
    holdings:
      @attributes:
        islocal: N