Acute Effects of Mechanical Insufflation-Exsufflation on the Breathing Pattern in Stable Subjects With Duchenne Muscular Dystrophy.

BACKGROUND: Duchenne muscular dystrophy (DMD) is characterized by progressive degeneration, wasting, and weakness of skeletal musculature, including respiratory muscles. Cough is also compromised with disease progression. Among cough-augmentation techniques, mechanical insufflation-exsufflation (MI-...

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Publicado en:Respiratory Care Vol. 63; no. 8; pp. 955 - 966
Autores principales: Cesareo, Ambra, LoMauro, Antonella, Santi, Marika, Biffi, Emilia, D'Angelo, Maria G., Aliverti, Andrea
Formato: CEU pictorial research tables/charts tracings Journal Article
Publicado: Mary Ann Liebert, Inc. Aug2018
Acceso en línea:Ver este registro en EBSCOhost
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      pub: Mary Ann Liebert, Inc.
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        atl: Acute Effects of Mechanical Insufflation-Exsufflation on the Breathing Pattern in Stable Subjects With Duchenne Muscular Dystrophy.
      aug:
        au:
          Cesareo, Ambra
          LoMauro, Antonella
          Santi, Marika
          Biffi, Emilia
          D'Angelo, Maria G.
          Aliverti, Andrea
        affil: Dipartimento di Elettronica, Informazione e Bioingegneria, Politecnico di Milano, Milan, Italy
      sug:
        subj:
          Insufflation
          Muscular Dystrophy, Duchenne
          Work of Breathing
          Human
          Plethysmography
          Respiratory Function Tests
          Male
          Female
          Adolescence
          Adult
          Descriptive Statistics
          Data Analysis Software
          Education, Continuing (Credit)
          Adolescent: 13-18 years
          Adult: 19-44 years
          Male
          Female
      ab: BACKGROUND: Duchenne muscular dystrophy (DMD) is characterized by progressive degeneration, wasting, and weakness of skeletal musculature, including respiratory muscles. Cough is also compromised with disease progression. Among cough-augmentation techniques, mechanical insufflation-exsufflation (MI-E) has demonstrated several clinical benefits in patients with chronic airway secretion obstruction and muscular weakness. In clinical practice, the use of MI-E in DMD patients is also suggested when they are stable with no airway infections. However, there is a paucity of studies that consider the effect of MI-E specifically on stable DMD patients who have adapted to the use of MI-E. METHODS: Twenty subjects with DMD with no active upper airway or lung infections, who used MI-E device regularly at home, were enrolled. They received a single MI-E treatment consisting of 5 cycles of 5 insufflations-exsufflations with their customary settings. Volume variations during quiet breathing, vital capacity, and cough before and after treatment were measured with optoelectronic plethysmography (OEP). RESULTS: A decrease in breathing frequency (P = .001) and the rapid shallow breathing index emerged (P = .007), while cough peak flow (Spirometer P = .86, OEP P = .58), vital capacity (Spirometer P = .78, OEP total chest wall P = .57), and end-expiratory volumes (Total chest wall P = .97, Ribcage P = .14, Abdomen P = .10) were not affected by the treatment. An increment of the chest wall volume variation during the expiratory cough phase was identified (P = .001), particularly due to an increase in abdominal expansion (P = .005). CONCLUSIONS: A single treatment of MI-E in subjects with stable DMD already adapted to the device can provide beneficial changes in breathing pattern through a significant decrease in breathing frequency and rapid shallow breathing. These findings suggest an improvement in short-term dyspnea, although there were no changes in lung-volume recruitment or unassisted cough peak flow.
      pubtype: Academic Journal
      doctype:
        CEU
        pictorial
        research
        tables/charts
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        Journal Article
      ougenre: Article
    language: English
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