Is SAPHO Syndrome Linked to PASH Syndrome and Hidradenitis Suppurativa by Nicastrin Mutation? A Case Report.
The SAPHO syndrome is a group of disorders that manifest as synovitis, acne, pustulosis, hyperostosis, and osteitis. Of these, acne damage can present as acne conglobata, acne fulminans, or hidradenitis suppurativa (HS).
| Publicado en: | Journal of Rheumatology Vol. 45; no. 8 |
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| Autores principales: | , , |
| Formato: | research Journal Article |
| Publicado: |
Journal of Rheumatology Publishing Co. Ltd.
Aug2018
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| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=131160408&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 131160408 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 0315162X 4CM jtl: Journal of Rheumatology issn: 0315162X maglogo: N pubinfo: dt: Aug2018 vid: 45 iid: 8 pid: 6803 pub: Journal of Rheumatology Publishing Co. Ltd. place: Toronto, Ontario artinfo: ui: 131160408 131160408 NLM30068763 131160408 10.3899/jrheum.171007 NLM30068763 131160408 ppct: 1 formats: tig: atl: Is SAPHO Syndrome Linked to PASH Syndrome and Hidradenitis Suppurativa by Nicastrin Mutation? A Case Report. aug: au: Li, Chengrang Xu, Haoxiang Wang, Baoxi affil: Institute of Dermatology, Chinese Academy of Medical Sciences and Peking Union Medical College, and Jiangsu Key Laboratory of Molecular Biology for Skin Diseases and STDs sug: subj: Membrane Glycoproteins Hidradenitis Suppurativa Acquired Hyperostosis Syndrome Peptide Hydrolases Acne Vulgaris Pyoderma Gangrenosum Male Adult Syndrome Human Validation Studies Comparative Studies Evaluation Research Multicenter Studies Adult: 19-44 years Male ab: The SAPHO syndrome is a group of disorders that manifest as synovitis, acne, pustulosis, hyperostosis, and osteitis. Of these, acne damage can present as acne conglobata, acne fulminans, or hidradenitis suppurativa (HS). pubtype: Academic Journal doctype: research Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
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