Imaging findings of sterile pyogenic arthritis, pyoderma gangrenosum and acne (PAPA) syndrome: differential diagnosis and review of the literature.

Pyogenic arthritis, pyoderma gangrenosum and acne (PAPA) syndrome is a rare autosomal-dominant autoinflammatory disease of incomplete penetrance and variable expression. PAPA syndrome is the result of a mutation in the proline serine threonine phosphatase-interacting protein 1 (PSTPIP1/CD2BP1) gene...

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Bibliographic Details
Published in:Pediatric Radiology Vol. 49; no. 1; pp. 23 - 37
Main Authors: Martinez-Rios, Claudia, Jariwala, Mehul P., Highmore, Kerri, Duffy, Karen Watanabe, Spiegel, Lynn, Laxer, Ronald M., Stimec, Jennifer
Format: diagnostic images review tables/charts Journal Article
Published: Springer Nature Jan2019
Online Access:View this record in EBSCOhost