PAPA and FMF in two siblings: possible amplification of clinical presentation? A case report.
Background: Familial Mediterranean Fever is a monogenic autoinflammatory disease, typically characterized by recurrent attacks of fever, serositis, aphthous of oral mucosa, erythema. "Pyogenic arthritis, pyoderma gangrenosum and acne syndrome" is a rare autoinflammatory disease with variable express...
| Publicado en: | Italian Journal of Pediatrics Vol. 45; no. 1 |
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| Autores principales: | , , , , |
| Formato: | case study Journal Article |
| Publicado: |
BioMed Central
8/23/2019
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| Acceso en línea: | Ver este registro en EBSCOhost |