Effect of Including Important Clinical Variables on Accuracy of the Lung Allocation Score for Cystic Fibrosis and Chronic Obstructive Pulmonary Disease.

Rationale: Clinical variables associated with shortened survival in patients with advanced-stage cystic fibrosis (CF) are not included in the lung allocation score (LAS).Objectives: To identify variables associated with wait-list and post-transplant mortality for CF lung transplant candidates using...

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Published in:American Journal of Respiratory & Critical Care Medicine Vol. 200; no. 8; pp. 1013 - 1022
Main Authors: Lehr, Carli J., Skeans, Melissa, Dasenbrook, Elliott, Fink, Aliza, Fernandez, Gabriela, Faro, Albert, Valapour, Maryam, Dasenbrook, Elliot C
Format: research Journal Article
Published: Oxford University Press / USA 10/15/2019
Online Access:View this record in EBSCOhost
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      dt: 10/15/2019
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      pub: Oxford University Press / USA
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        10.1164/rccm.201902-0252OC
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        atl: Effect of Including Important Clinical Variables on Accuracy of the Lung Allocation Score for Cystic Fibrosis and Chronic Obstructive Pulmonary Disease.
      aug:
        au:
          Lehr, Carli J.
          Skeans, Melissa
          Dasenbrook, Elliott
          Fink, Aliza
          Fernandez, Gabriela
          Faro, Albert
          Valapour, Maryam
          Dasenbrook, Elliot C
        affil: Cleveland Clinic, Cleveland, Ohio.
      sug:
        subj:
          Algorithms
          Organ Procurement Standards
          Patient Selection
          Cystic Fibrosis Diagnosis
          Waiting Lists
          Lung Transplantation Standards
          Pulmonary Disease, Chronic Obstructive Diagnosis
          Cystic Fibrosis Physiopathology
          Aged, 80 and Over
          Cox Proportional Hazards Model
          Adult
          Severity of Illness Indices
          Female
          Middle Age
          Aged
          Retrospective Design
          Child
          Pulmonary Disease, Chronic Obstructive Physiopathology
          Young Adult
          Male
          Practice Guidelines
          Human
          Reproducibility of Results
          Adolescence
          Validation Studies
          Comparative Studies
          Evaluation Research
          Multicenter Studies
          Aged, 80 & over
          Adult: 19-44 years
          Middle Aged: 45-64 years
          Aged: 65+ years
          Child: 6-12 years
          Adolescent: 13-18 years
          Female
          Male
      ab: Rationale: Clinical variables associated with shortened survival in patients with advanced-stage cystic fibrosis (CF) are not included in the lung allocation score (LAS).Objectives: To identify variables associated with wait-list and post-transplant mortality for CF lung transplant candidates using a novel database and to analyze the impact of including new CF-specific variables in the LAS system.Methods: A deterministic matching algorithm identified patients from the Scientific Registry of Transplant Recipients and the Cystic Fibrosis Foundation Patient Registry. LAS wait-list and post-transplant survival models were recalculated using CF-specific variables. This multicenter, retrospective, population-based study of all lung transplant wait-list candidates aged 12 years or older from January 1, 2011, to December 31, 2014, included 9,043 patients on the lung transplant waiting list and 6,110 lung transplant recipients between 2011 and 2014, comprising 1,020 and 677 with CF, respectively.Measurements and Main Results: Measured outcomes were changes in LAS and lung allocation rank. For CF candidates, any Burkholderia sp. (hazard ratio [HR], 2.8; 95% confidence interval [CI], 1.2-6.6), 29-42 days hospitalized (HR 2.8; CI 1.3-5.9), massive hemoptysis (HR 2.1; CI 1.1-3.9), and relative drop in FEV1 ≥30% over 12 months (HR 1.7; CI 1.0-2.8) increased wait-list mortality risk; pulmonary exacerbation time 15-28 days (1.8; 1.1-2.9) increased post-transplant mortality risk. A relative drop in FEV1 ≥10% in chronic obstructive pulmonary disease (COPD) candidates was associated with increased wait-list mortality risk (HR 2.6; CI 1.2-5.4). Variability in LAS score and rank increased in patients with CF. Priority for transplant increased for COPD candidates. Access did not change for other diagnosis groups.Conclusions: Adding CF-specific variables improved discrimination among wait-listed CF candidates and benefited COPD candidates.
      pubtype: Academic Journal
      doctype:
        research
        Journal Article
      ougenre: Article
    language: English
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