Autoinflammatory diseases in childhood, part 1: monogenic syndromes.

Autoinflammatory diseases constitute a family of disorders defined by aberrant stimulation of inflammatory pathways without involving antigen-directed autoimmunity. They may be divided into monogenic and polygenic types. Monogenic autoinflammatory syndromes are those with identified genetic mutation...

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Detalles Bibliográficos
Publicado en:Pediatric Radiology Vol. 50; no. 3; pp. 415 - 431
Autores principales: Navallas, María, Inarejos Clemente, Emilio J., Iglesias, Estíbaliz, Rebollo-Polo, Mónica, Zaki, Faizah Mohd, Navarro, Oscar M.
Formato: review Journal Article
Publicado: Springer Nature Mar2020
Acceso en línea:Ver este registro en EBSCOhost