Choroidal Thickness in Different Types of Inherited Retinal Dystrophies.

Purpose: To compare the choroidal thickness among eyes with retinitis pigmentosa (RP), Stargardt disease, Usher syndrome, cone-rod dystrophy, and healthy eyes of sex- and age-matched individuals. Methods: In this comparative study, 503 eyes with RP (n = 264), cone-rod dystrophy (n = 109), Stargardt...

Descripción completa

Detalles Bibliográficos
Publicado en:Journal of Ophthalmic & Vision Research Vol. 15; no. 3; pp. 351 - 362
Autores principales: Sabbaghi, Hamideh, Ahmadieh, Hamid, Jalili, Jalil, Behnaz, Nazanin, Fakhri, Maryam, Suri, Fatemeh, Kheiri, Bahareh, Rajabpour, Mojtaba, Entezari, Morteza, Daftarian, Narsis
Formato: diagnostic images research tables/charts Journal Article
Publicado: Knowledge E DMCC 2020
Acceso en línea:Ver este registro en EBSCOhost
fields @attributes:
  recordID: 1
pdfLink:
plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=145161949&site=ehost-live
header:
  @attributes:
    shortDbName: ccm
    uiTerm: 145161949
    longDbName: CINAHL Complete
    uiTag: AN
  controlInfo:
    bkinfo:
    dissinfo:
    jinfo:
      jid:
        20082010
        AY5S
      jtl: Journal of Ophthalmic & Vision Research
      issn: 20082010
      maglogo: N
    pubinfo:
      dt: 2020
      vid: 15
      iid: 3
      pid: 35682
      pub: Knowledge E DMCC
    artinfo:
      ui:
        145161949
        145161949
        145161949
        10.18502/jovr.v15i3.7454
        145161949
      ppf: 351
      ppct: 11
      formats:
        fmt:
          @attributes:
            type: P
      tig:
        atl: Choroidal Thickness in Different Types of Inherited Retinal Dystrophies.
      aug:
        au:
          Sabbaghi, Hamideh
          Ahmadieh, Hamid
          Jalili, Jalil
          Behnaz, Nazanin
          Fakhri, Maryam
          Suri, Fatemeh
          Kheiri, Bahareh
          Rajabpour, Mojtaba
          Entezari, Morteza
          Daftarian, Narsis
        affil: Ophthalmic Epidemiology Research Center, Research Institute for Ophthalmology and Vision Science, Shahid Beheshti University of Medical Sciences, Tehran, Iran
      sug:
        subj:
          Uvea Pathology
          Eye Diseases, Hereditary Physiopathology
          Retinitis Pigmentosa Physiopathology
          Stargardt Disease Physiopathology
          Usher's Syndrome Physiopathology
          Cone-Rod Dystrophies Physiopathology
          Age Factors
          Sex Factors
          Human
          Comparative Studies
          Tomography, Optical Coherence Methods
          Data Analysis Software
          Adult
          Descriptive Statistics
          Child, Preschool
          Child
          Adolescence
          Middle Age
          Aged
          Adult: 19-44 years
          Child, Preschool: 2-5 years
          Child: 6-12 years
          Adolescent: 13-18 years
          Middle Aged: 45-64 years
          Aged: 65+ years
      ab: Purpose: To compare the choroidal thickness among eyes with retinitis pigmentosa (RP), Stargardt disease, Usher syndrome, cone-rod dystrophy, and healthy eyes of sex- and age-matched individuals. Methods: In this comparative study, 503 eyes with RP (n = 264), cone-rod dystrophy (n = 109), Stargardt disease (n = 76), and Usher syndrome (n = 54) were included. To validate the data, 109 healthy eyes of 56 sex- and age-matched individuals were studied as controls. Choroidal imaging was performed using enhanced depth imaging-optical coherence tomography. Choroidal thickness was measured manually using MATLAB software at 13 points in nasal and temporal directions from the foveal center with the interval of 500 pm and the choroidal area encompassing the measured points was calculated automatically. Results: The mean age was 36.33 ± 13.07 years (range, 5 to 72 years). The mean choroidal thickness at 13 points of the control eyes was statistically significantly higher than that in eyes with RP (P < 0.001) and Usher syndrome (P < 0.05), but not significantly different from that in eyes with Stargardt disease and cone-rod dystrophy. Among different inherited retinal dystrophies (IRDs), the choroidal thickness was the lowest in eyes with RP (P < 0.001). Choroidal thickness in the subfoveal area correlated negatively with best-corrected visual acuity (r = -0.264, P < 0.001) and the duration of ocular symptoms (r = -0.341, P < 0.001) in all studied IRDs. No significant correlation was observed between the subfoveal choroidal thickness and central macular thickness (r = -0.24, P = 0.576). Conclusion: Choroidal thinning in four different types of IRDs does not follow a similar pattern and depends on the type of IRD and the duration of ocular symptoms. A larger cohort is required to verify these findings.
      pubtype: Academic Journal
      doctype:
        diagnostic images
        research
        tables/charts
        Journal Article
      ougenre: Article
    language: English
    refInfo:
    holdings:
      @attributes:
        islocal: N