Approaches to studying the genomic architecture of complex birth defects.

Every year nearly 6 percent of children worldwide are born with a serious congenital malformation, resulting in death or lifelong disability. In the United States, birth defects remain one of the leading causes of infant mortality. Among the common structural congenital defects are conditions known...

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Publicado en:Prenatal Diagnosis Vol. 40; no. 9; pp. 1047 - 1056
Autores principales: Taiwo, Toluwani E., Cao, Xuanye, Cabrera, Robert M., Lei, Yunping, Finnell, Richard H.
Formato: review Journal Article
Publicado: Wiley-Blackwell Aug2020
Acceso en línea:Ver este registro en EBSCOhost
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      dt: Aug2020
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      pub: Wiley-Blackwell
      place: Malden, Massachusetts
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        atl: Approaches to studying the genomic architecture of complex birth defects.
      aug:
        au:
          Taiwo, Toluwani E.
          Cao, Xuanye
          Cabrera, Robert M.
          Lei, Yunping
          Finnell, Richard H.
        affil: Rice University, Houston Texas, USA
      sug:
        subj:
          Neural Tube Defects
          Genomics Methods
          Female
          Prenatal Exposure Delayed Effects
          Embryonic Structures Metabolism
          Animals
          Embryonic Structures
          Abnormalities Etiology
          Anticonvulsants Adverse Effects
          Pregnancy
          Neural Tube Defects Epidemiology
          Fetal Development
          Abnormalities Epidemiology
          Genomics Trends
          Models, Biological
          Abnormalities
          Clinical Assessment Tools
          Scales
          Questionnaires
          Female
      ab: Every year nearly 6 percent of children worldwide are born with a serious congenital malformation, resulting in death or lifelong disability. In the United States, birth defects remain one of the leading causes of infant mortality. Among the common structural congenital defects are conditions known as neural tube defects (NTDs). These are a class of malformation of the brain and spinal cord where the neural tube fails to close during the neurulation. Although NTDs remain among the most pervasive and debilitating of all human developmental anomalies, there is insufficient understanding of their etiology. Previous studies have proposed that complex birth defects like NTDs are likely omnigenic, involving interconnected gene regulatory networks with associated signals throughout the genome. Advances in technologies have allowed researchers to more critically investigate regulatory gene networks in ever increasing detail, informing our understanding of the genetic basis of NTDs. Employing a systematic analysis of these complex birth defects using massively parallel DNA sequencing with stringent bioinformatic algorithms, it is possible to approach a greater level of understanding of the genomic architecture underlying NTDs. Herein, we present a brief overview of different approaches undertaken in our laboratory to dissect out the genetics of susceptibility to NTDs. This involves the use of mouse models to identify candidate genes, as well as large scale whole genome/whole exome (WGS/WES) studies to interrogate the genomic landscape of NTDs. The goal of this research is to elucidate the gene-environment interactions contributing to NTDs, thus encouraging global research efforts in their prevention.
      pubtype: Academic Journal
      doctype:
        review
        Journal Article
      ougenre: Article
    language: English
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