Specific temperament in patients with nevoid basal cell carcinoma syndrome.

Background: Nevoid basal cell carcinoma syndrome (NBCCS) is a neurocutaneous disease, characterized by tumorigenesis and developmental anomalies due to aberrant sonic hedgehog (Shh) signaling. Patients with NBCCS typically appear calm and carefree, suggesting that a specific personality in these pat...

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Detalles Bibliográficos
Publicado en:Pediatrics International Vol. 63; no. 2; pp. 177 - 183
Autores principales: Uchikawa, Hideki, Fujii, Katsunori, Shiohama, Tadashi, Nakazato, Michiko, Shimizu, Eiji, Miyashita, Toshiyuki, Shimojo, Naoki
Formato: diagnostic images research tables/charts Journal Article
Publicado: Wiley-Blackwell Feb2021
Acceso en línea:Ver este registro en EBSCOhost