Similar but different: distinguishing between pemphigus vegetans and pyostomatitis-pyodermatitis vegetans.

A 51-year-old woman presented with a 4-month history of painful ulcers in the mouth and vulva, and painful vegetative plaques at intertriginous sites. Skin biopsies showed squamous hyperplasia and intraepidermal eosinophilic pustulation. Skin direct immunofluorescence (DIF) revealed intercellular de...

Descripción completa

Detalles Bibliográficos
Publicado en:BMJ Case Reports Vol. 14; no. 4; pp. 1 - 4
Autores principales: Stagg, Brendan, Simpson, Anna, Sidhu, Shireen
Formato: Journal Article
Publicado: BMJ Publishing Group Apr2021
Acceso en línea:Ver este registro en EBSCOhost
fields @attributes:
  recordID: 1
pdfLink:
plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=150456528&site=ehost-live
header:
  @attributes:
    shortDbName: ccm
    uiTerm: 150456528
    longDbName: CINAHL Complete
    uiTag: AN
  controlInfo:
    bkinfo:
    dissinfo:
    jinfo:
      jid:
        1757790X
        B755
      jtl: BMJ Case Reports
      issn: 1757790X
      maglogo: N
    pubinfo:
      dt: Apr2021
      vid: 14
      iid: 4
      pid: 8280
      pub: BMJ Publishing Group
    artinfo:
      ui:
        150456528
        10.1136/bcr-2021-242162
        150456528
      ppf: 1
      ppct: 3
      formats:
      tig:
        atl: Similar but different: distinguishing between pemphigus vegetans and pyostomatitis-pyodermatitis vegetans.
      aug:
        au:
          Stagg, Brendan
          Simpson, Anna
          Sidhu, Shireen
        affil: SA Health, Adelaide, South Australia, Australia.
      sug:
      ab: A 51-year-old woman presented with a 4-month history of painful ulcers in the mouth and vulva, and painful vegetative plaques at intertriginous sites. Skin biopsies showed squamous hyperplasia and intraepidermal eosinophilic pustulation. Skin direct immunofluorescence (DIF) revealed intercellular deposition of IgG and C3 in the lower part of the epidermis, while serum indirect immunofluorescence (IIF) confirmed the presence of antiepithelial antibodies. The patient was diagnosed with pemphigus vegetans, and successfully treated with dapsone, prednisolone and topical steroids. Although pemphigus vegetans and pyostomatitispyodermatitis vegetans can show identical clinical and histological features, the presence or absence of comorbid inflammatory bowel disease, and the results of both skin DIF and serum IIF can be used to distinguish between these two conditions. This case report explores the challenges in making this distinction, and the implications of establishing the correct diagnosis.
      pubtype: Academic Journal
      doctype: Journal Article
      ougenre: Article
    language: English
    refInfo:
    holdings:
      @attributes:
        islocal: N