Clinical features and diagnostic tools in idiopathic inflammatory myopathies.
Idiopathic inflammatory myopathies (IIMs) are rare autoimmune disorders affecting primarily muscles, but other organs can be involved. This review describes the clinical features, diagnosis and treatment for IIMs, namely polymyositis (PM), dermatomyositis (DM), sporadic inclusion body myositis (sIBM...
| Publicado en: | Critical Reviews in Clinical Laboratory Sciences Vol. 59; no. 4; pp. 219 - 241 |
|---|---|
| Autores principales: | , , , , , , , |
| Formato: | algorithm pictorial review tables/charts Journal Article |
| Publicado: |
Taylor & Francis Ltd
Jun2022
|
| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=156966125&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 156966125 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 10408363 1AV jtl: Critical Reviews in Clinical Laboratory Sciences issn: 10408363 maglogo: Y pubinfo: dt: Jun2022 vid: 59 iid: 4 pid: 377 pub: Taylor & Francis Ltd place: Philadelphia, Pennsylvania artinfo: ui: 156966125 153516025 156966125 156966125 10.1080/10408363.2021.2000584 156966125 ppf: 219 ppct: 22 formats: fmt: – @attributes: type: T – @attributes: type: P tig: atl: Clinical features and diagnostic tools in idiopathic inflammatory myopathies. aug: au: Tsamis, Konstantinos I. Boutsoras, Constantinos Kaltsonoudis, Evripidis Pelechas, Eleftherios Nikas, Ilias P. Simos, Yannis V. Voulgari, Paraskevi V. Sarmas, Ioannis affil: Department of Neurology, University Hospital of Ioannina, Ioannina, Greece sug: subj: Myositis Symptoms Myositis Diagnosis Myositis Therapy Rare Diseases Autoantibodies Multidisciplinary Care Team Immunoenzyme Techniques ab: Idiopathic inflammatory myopathies (IIMs) are rare autoimmune disorders affecting primarily muscles, but other organs can be involved. This review describes the clinical features, diagnosis and treatment for IIMs, namely polymyositis (PM), dermatomyositis (DM), sporadic inclusion body myositis (sIBM), immune-mediated necrotizing myopathy (IMNM), and myositis associated with antisynthetase syndrome (ASS). The diagnostic approach has been updated recently based on the discovery of circulating autoantibodies, which has enhanced the management of patients. Currently, validated classification criteria for IIMs allow clinical studies with well-defined sets of patients but diagnostic criteria to guide the care of individual patients in routine clinical practice are still missing. This review analyzes the clinical manifestations and laboratory findings of IIMs, discusses the efficiency of modern and standard methods employed in their workup, and delineates optimal practice for clinical care. Α multidisciplinary diagnostic approach that combines clinical, neurologic and rheumatologic examination, evaluation of electrophysiologic and morphologic muscle characteristics, and assessment of autoantibody immunoassays has been determined to be the preferred approach for effective management of patients with suspected IIMs. pubtype: Academic Journal doctype: algorithm pictorial review tables/charts Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
|---|