Nutcracker syndrome: a potentially underdiagnosed cause of proteinuria in children with familial Mediterranean fever.

Introduction: Familial Mediterranean fever (FMF) is the most common hereditary autoinflammatory disease with an increased risk for secondary amyloidosis. Since lifelong colchicine has been the treatment of choice that prevents renal amyloidosis, non-amyloid kidney diseases are more frequently consid...

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Publicado en:Pediatric Nephrology Vol. 37; no. 7; pp. 1615 - 1622
Autores principales: Avar-Aydin, Pinar Ozge, Ozcakar, Zeynep Birsin, Cakar, Nilgun, Fitoz, Suat, Karakas, Hatice Dilara, Yalcinkaya, Fatos
Formato: research tables/charts Journal Article
Publicado: Springer Nature Jul2022
Acceso en línea:Ver este registro en EBSCOhost