SAPHO Syndrome Presenting With Atlo-Epistrophic Synovitis and Left Vocal Cord Paresis: A Challenging Diagnosis.
SAPHO (synovitis, acne, pustulosis, hyperostosis, and osteitis) is a rare syndrome mainly characterized by cutaneous and osteoarticular manifestations. The most typical osteoarticular manifestations are localized to the anterior chest wall and include a usually noninfectious osteitis, hyperostosis,...
| Publicado en: | Clinical Medicine Insights: Arthritis & Musculoskeletal Disorders pp. 1 - 10 |
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| Autores principales: | , , , , , |
| Formato: | case study diagnostic images pictorial Journal Article |
| Publicado: |
Sage Publications Inc.
9/7/2022
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| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=158991772&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 158991772 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 11795441 B3KJ jtl: Clinical Medicine Insights: Arthritis & Musculoskeletal Disorders issn: 11795441 maglogo: Y pubinfo: dt: 9/7/2022 pid: 20732 pub: Sage Publications Inc. place: Thousand Oaks, California artinfo: ui: 158991772 158991772 158991772 10.1177/11795441221118918 158991772 ppf: 1 ppct: 9 formats: fmt: – @attributes: type: T – @attributes: type: P tig: atl: SAPHO Syndrome Presenting With Atlo-Epistrophic Synovitis and Left Vocal Cord Paresis: A Challenging Diagnosis. aug: au: Maranini, Beatrice Ciancio, Giovanni Rinaldi, Rosa Borrelli, Massimo Pugliatti, Maura Govoni, Marcello affil: Rheumatology Unit, Department of Medical Sciences, University of Ferrara, Ferrara, Italy sug: subj: Acquired Hyperostosis Syndrome Diagnosis Acquired Hyperostosis Syndrome Symptoms Synovitis Etiology Vocal Cord Paralysis Etiology Atlanto-Axial Joint Pathology Osteolysis Etiology Neck Pain Etiology Skin Manifestations ab: SAPHO (synovitis, acne, pustulosis, hyperostosis, and osteitis) is a rare syndrome mainly characterized by cutaneous and osteoarticular manifestations. The most typical osteoarticular manifestations are localized to the anterior chest wall and include a usually noninfectious osteitis, hyperostosis, and synovitis of the sternoclavicular joints. However, clinical presentation of SAPHO syndrome can be quite heterogeneous. Several clinical and radiological features are shared with other well-defined pathological entities, and clinical signs and symptoms often occur at different timepoints. Mainly due to this complexity and its rarity, there are currently no validated diagnostic criteria for SAPHO syndrome. Inflammation of the soft tissues around the bones and possible nerve compression could contribute to dysphagia, hypophonia, or obstruction of the airways. Neurologic manifestations could therefore be part of this multiorgan involvement. Here, we present a case of SAPHO syndrome with atypical onset symptoms, characterized by left vocal cord paralysis, acute neck pain due to osteolytic atlantoepistrophic lesion, and an unusual cutaneous manifestation, diagnosed as mid-dermal elastolysis. The latest two, to the best of our knowledge, have been here first described in a case of SAPHO syndrome. pubtype: Academic Journal doctype: case study diagnostic images pictorial Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
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