An In Silico Cardiomyocyte Reveals the Impact of Changes in CaMKII Signalling on Cardiomyocyte Contraction Kinetics in Hypertrophic Cardiomyopathy.

Hypertrophic cardiomyopathy (HCM) is characterised by asymmetric left ventricular hypertrophy, ventricular arrhythmias, and cardiomyocyte dysfunction that may cause sudden death. HCM is associated with mutations in sarcomeric proteins and is usually transmitted as an autosomal-dominant trait. The ai...

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Publicado en:BioMed Research International Vol. 2024; pp. 1 - 15
Autores principales: Adeniran, Ismail, Wadee, Hafsa, Degens, Hans
Formato: equations & formulas pictorial research tables/charts Journal Article
Publicado: Wiley-Blackwell 3/25/2024
Acceso en línea:Ver este registro en EBSCOhost
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      jtl: BioMed Research International
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    pubinfo:
      dt: 3/25/2024
      vid: 2024
      pid: 480
      pub: Wiley-Blackwell
      place: Malden, Massachusetts
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        176216134
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        10.1155/2024/6160554
        176216134
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        atl: An In Silico Cardiomyocyte Reveals the Impact of Changes in CaMKII Signalling on Cardiomyocyte Contraction Kinetics in Hypertrophic Cardiomyopathy.
      aug:
        au:
          Adeniran, Ismail
          Wadee, Hafsa
          Degens, Hans
        affil: Centre for Advanced Computational Science, Manchester Metropolitan University, Manchester M15 6BH, UK
      sug:
        subj:
          Cardiomyopathy, Hypertrophic Physiopathology
          Myocardial Contraction
          Kinetics
          Signal Transduction
          Myocytes, Cardiac
          Phosphotransferases Metabolism
          Electrophysiology
          Energy Metabolism
          Human
          Models, Biological
          Ion Channels
          Calcium Binding Proteins
          Simulations
          Phosphocreatine
          Adenosine Triphosphate
          Descriptive Statistics
      ab: Hypertrophic cardiomyopathy (HCM) is characterised by asymmetric left ventricular hypertrophy, ventricular arrhythmias, and cardiomyocyte dysfunction that may cause sudden death. HCM is associated with mutations in sarcomeric proteins and is usually transmitted as an autosomal-dominant trait. The aim of this in silico study was to assess the mechanisms that underlie the altered electrophysiological activity, contractility, regulation of energy metabolism, and crossbridge cycling in HCM at the single-cell level. To investigate this, we developed a human ventricular cardiomyocyte model that incorporates electrophysiology, metabolism, and force generation. The model was validated by its ability to reproduce the experimentally observed kinetic properties of human HCM induced by (a) remodelling of several ion channels and Ca2+-handling proteins arising from altered Ca2+/calmodulin kinase II signalling pathways and (b) increased Ca2+ sensitivity of the myofilament proteins. Our simulation showed a decreased phosphocreatine-to-ATP ratio (-9%) suggesting a negative mismatch between energy expenditure and supply. Using a spatial myofilament half-sarcomere model, we also compared the fraction of detached, weakly bound, and strongly bound crossbridges in the control and HCM conditions. Our simulations showed that HCM has more crossbridges in force-producing states than in the control condition. In conclusion, our model reveals that impaired crossbridge kinetics is accompanied by a negative mismatch between the ATP supply and demand ratio. This suggests that improving this ratio may reduce the incidence of sudden death in HCM.
      pubtype: Academic Journal
      doctype:
        equations & formulas
        pictorial
        research
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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