Cystic fibrosis liver disease.

Cystic fibrosis (CF) is an inherited autosomal recessive disease that affects exocrine systems including sinuses, lungs, pancreas, liver, skin, gastrointestinal tract, and reproductive tract. The effects on the liver ranges from elevated liver function tests to cirrhosis and liver failure. The labor...

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Publicado en:Journal of Pain Management Vol. 16; no. 3; pp. 195 - 216
Autor principal: Barr, Jayne A.
Formato: tables/charts Journal Article
Publicado: Nova Science Publishers, Inc. 2023
Acceso en línea:Ver este registro en EBSCOhost
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      dt: 2023
      vid: 16
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      pub: Nova Science Publishers, Inc.
      place: Hauppauge, New York
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        atl: Cystic fibrosis liver disease.
      aug:
        au: Barr, Jayne A.
        affil: Internal Medicine, Department of Internal Medicine, MetroHealth Case Western Reserve University, Cleveland, Ohio, USA
      sug:
        subj:
          Cystic Fibrosis
          Liver Diseases
          Lung Diseases
          Pancreas Pathology
          Skin Diseases
          Gastrointestinal System Pathology
          Genital Diseases
          Liver Transplantation
          Quality of Life
          Quality Improvement
          Life Expectancy
      ab: Cystic fibrosis (CF) is an inherited autosomal recessive disease that affects exocrine systems including sinuses, lungs, pancreas, liver, skin, gastrointestinal tract, and reproductive tract. The effects on the liver ranges from elevated liver function tests to cirrhosis and liver failure. The laboratory and radiographic screening, treatment alternatives, and organ transplantation are important aspects in the care of CF patients. Liver transplant and lung-liver transplant can improve the quality of life and life expectancy. Optimal timing for referral for liver transplantation remains controversial. Future research of cystic fibrosis liver disease continues to focus on the CFTR defect, genetic modifiers, and the biliary bicarbonate exchange.
      pubtype: Academic Journal
      doctype:
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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