Development of a Multiplexed Sphingolipids Method for Diagnosis of Inborn Errors of Ceramide Metabolism.

Background Sphingolipids play a crucial role in cellular functions and are essential components of cell membranes, signaling molecules, and lipid metabolism. In particular, ceramide is a key intermediate in sphingolipid metabolism and defects in ceramide metabolism can lead to various inborn errors...

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Publicado en:Clinical Chemistry Vol. 70; no. 11; pp. 1366 - 1375
Autores principales: Byeon, Seul Kee, Kim, Jinyong, Wegwerth, Peter Jared, Zenka, Roman, George, John P, Vairo, Filippo Pinto e, Oglesbee, Devin, Schultz, Matthew J, Matern, Dietrich, Pandey, Akhilesh
Formato: Journal Article
Publicado: Oxford University Press / USA Nov2024
Acceso en línea:Ver este registro en EBSCOhost