Refractory pyoderma gangrenosum-like ulcerations in granulomatosis with polyangiitis treated successfully with rituximab.

Granulomatosis with polyangiitis (GPA) is a small-to- medium vessel vasculitis that can affect the skin, respiratory tract, kidneys and other organs. A rare cutaneous manifestation of GPA is pyoderma gangrenosum (PG)-like ulcerations, which can have debilitating and disfiguring consequences. We repo...

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Publicado en:BMJ Case Reports Vol. 18; no. 1; pp. 1 - 4
Autores principales: Tran, Vanessa, Chatfield, Simon, Ramirez, Ann, Scardamaglia, Laura
Formato: Journal Article
Publicado: BMJ Publishing Group Jan2025
Acceso en línea:Ver este registro en EBSCOhost
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      dt: Jan2025
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        10.1136/bcr-2024-262584
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        atl: Refractory pyoderma gangrenosum-like ulcerations in granulomatosis with polyangiitis treated successfully with rituximab.
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        au:
          Tran, Vanessa
          Chatfield, Simon
          Ramirez, Ann
          Scardamaglia, Laura
        affil: Dermatology, The Royal Melbourne Hospital, Parkville, Victoria, Australia.
      sug:
      ab: Granulomatosis with polyangiitis (GPA) is a small-to- medium vessel vasculitis that can affect the skin, respiratory tract, kidneys and other organs. A rare cutaneous manifestation of GPA is pyoderma gangrenosum (PG)-like ulcerations, which can have debilitating and disfiguring consequences. We report the case of a man in his 40s with refractory PG-like ulcerations secondary to GPA, not responsive to conventional immunosuppression, who was successfully treated with rituximab. This case emphasises the need for early recognition of this rare manifestation to allow for prompt initiation of treatment.
      pubtype: Academic Journal
      doctype: Journal Article
      ougenre: Article
    language: English
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