Increased Global Post‐Systolic Contraction During 1st Interstage Predicts Medium‐Term Death or Transplantation in Children With Hypoplastic Left Heart Syndrome.

Background: Echocardiography parameters of right ventricular (RV) dysfunction, fractional area change (RVFAC), and global longitudinal strain during the first interstage have been shown to be associated with death or transplantation in patients with HLHS. However, both parameters lack adequate discr...

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Published in:Echocardiography Vol. 42; no. 7; pp. 1 - 9
Main Authors: Harake, Danielle, Kapravelou, Eva, Eckersley, Luke, Tham, Edythe, Colen, Timothy, Lin, Lily, Shigemitsu, Sachie, Beigh, Mirza, Moray, Amol, Khoo, Nee Scze
Format: diagnostic images research tables/charts Journal Article
Published: Wiley-Blackwell Jul2025
Online Access:View this record in EBSCOhost
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      pub: Wiley-Blackwell
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        10.1111/echo.70244
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        atl: Increased Global Post‐Systolic Contraction During 1st Interstage Predicts Medium‐Term Death or Transplantation in Children With Hypoplastic Left Heart Syndrome.
      aug:
        au:
          Harake, Danielle
          Kapravelou, Eva
          Eckersley, Luke
          Tham, Edythe
          Colen, Timothy
          Lin, Lily
          Shigemitsu, Sachie
          Beigh, Mirza
          Moray, Amol
          Khoo, Nee Scze
        affil: Stollery Children's Hospital and University of Alberta, Edmonton, Canada
      sug:
        subj:
          Hypoplastic Left Heart Syndrome Surgery
          Heart Transplantation
          Heart Conduction System Physiopathology
          Death Risk Factors
          Risk Assessment
          Human
          Descriptive Statistics
          Data Analysis Software
          Post Hoc Analysis
          Mann-Whitney U Test
          Kaplan-Meier Estimator
          Spearman's Rank Correlation Coefficient
          Confidence Intervals
          Log-Rank Test
          Prospective Studies
          Male
          Female
          Infant
          Infant: 1-23 months
          Male
          Female
      ab: Background: Echocardiography parameters of right ventricular (RV) dysfunction, fractional area change (RVFAC), and global longitudinal strain during the first interstage have been shown to be associated with death or transplantation in patients with HLHS. However, both parameters lack adequate discriminatory characteristics. This study sought to examine global post‐systolic contraction (PSC), a marker of myocardial inefficiency, as a predictor of death or transplantation (Tx) in patients with classic hypoplastic left heart syndrome (HLHS). Methods: We performed a post‐hoc analysis of 62 prospectively recruited patients with HLHS prior to the bidirectional cavopulmonary anastomosis (BCPA) surgery. We measured RV function parameters: RVFAC, global longitudinal strain, strain rate, mechanical dispersion index (MDI), and PSC. For each parameter, the receiver operating characteristic analysis determined the optimal cut‐offs for the primary endpoint of death/Tx, followed by a Kaplan‐Meier analysis. Parameters interobserver variability testing was performed. Results: Median follow‐up from pre‐BCPA echocardiogram was 7.4 years. HLHS with outcome of death/Tx (n = 14) had lower RVFAC, longitudinal strain and strain rate, and increased PSC when compared with survivors. PSC of >5% performed the best, with the greatest area under the curve 0.75, sensitivity 64% and specificity 83%, hazard ratio 5.54 (95% CI 1.63–18.66), for the primary endpoint of death/Tx. PSC and strain parameters had excellent reproducibility. Conclusion: Increased global post‐systolic contraction during the first interstage is associated with an outcome of death or transplantation in the medium term follow up of patients with HLHS. PSC has a greater specificity and reproducibility than global longitudinal strain and RV FAC. Investigation into its use in clinical practice as a predictor of outcome is warranted.
      pubtype: Academic Journal
      doctype:
        diagnostic images
        research
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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