Echocardiographic Nomogram Model: A Tool for Assessing Cardiac Involvement in Patients With Systemic Amyloidosis.

Objectives: Cardiac involvement is significantly relevant to a poor prognosis in patients with systemic amyloidosis, often leading to adverse outcomes. The objective of this study was to develop a diagnostic model for cardiac amyloidosis (CA) in primary light chain amyloidosis (pAL) to facilitate ea...

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Publicado en:Echocardiography Vol. 42; no. 8; pp. 1 - 10
Autores principales: Lin, Qiongwen, Li, Xiaoshan, Tan, Zekun, Xu, Ruixue, Fei, Hongwen, Chen, Oudi
Formato: diagnostic images research tables/charts Journal Article
Publicado: Wiley-Blackwell Aug2025
Acceso en línea:Ver este registro en EBSCOhost
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      pub: Wiley-Blackwell
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        atl: Echocardiographic Nomogram Model: A Tool for Assessing Cardiac Involvement in Patients With Systemic Amyloidosis.
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          Lin, Qiongwen
          Li, Xiaoshan
          Tan, Zekun
          Xu, Ruixue
          Fei, Hongwen
          Chen, Oudi
        affil: Guangdong Cardiovascular Institute, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou Guangdong Province, , China
      sug:
        subj:
          Heart Pathology
          Amyloidosis Prognosis
          Amyloidosis Complications
          Amyloidosis Radiography
          Echocardiography Methods
          Prediction Models
          Early Diagnosis
          Human
          Male
          Female
          Middle Age
          Aged
          Retrospective Design
          Record Review
          Magnetic Resonance Imaging Methods
          Risk Assessment
          Univariate Statistics
          Logistic Regression
          Random Forest
          Algorithms
          ROC Curve
          Sensitivity and Specificity
          Predictive Value of Tests
          Cardiac Output
          Ventricular Function
          Confidence Intervals
          T-Tests
          Data Analysis Software
          Descriptive Statistics
          Funding Source
          Middle Aged: 45-64 years
          Aged: 65+ years
          Male
          Female
      ab: Objectives: Cardiac involvement is significantly relevant to a poor prognosis in patients with systemic amyloidosis, often leading to adverse outcomes. The objective of this study was to develop a diagnostic model for cardiac amyloidosis (CA) in primary light chain amyloidosis (pAL) to facilitate early detection and improve prognostic evaluation. Methods: In this retrospective study involving 72 patients with primary pAL amyloidosis (51 with cardiac involvement), we systematically employed cardiac magnetic resonance imaging (CMR) for cardiac assessment. CA diagnosis was confirmed histologically via noncardiac tissue biopsy, positive for light chain systemic amyloidosis. To dissect the risk factors for cardiac involvement, we applied both univariate logistic regression and a random forest algorithm. Subsequently, the findings from these analyses informed the construction of a predictive nomogram. We rigorously evaluated the nomogram's performance using receiver operating characteristic curve analysis, calibration curve assessment, and decision curve analysis. Results: The nomogram model included relative wall thickness (RWT), the ratio of mitral peak flow velocity in early diastolic (E wave) to the pulsed tissue Doppler imaging‐derived early diastolic peak velocity (e′ wave) at the interventricular septal mitral annulus (E/e′ sep), ejection fraction to peak systolic global longitudinal strain ratio (EFSR) and right ventricular fractional area change (RV FAC). The model exhibited good diagnostic performance, with an area under the ROC curve of 0.85 (95% CI, 0.75–0.92), a sensitivity of 80.4% (95% CI, 66.9%–90.2%), and a specificity of 85.7% (95% CI, 63.7%–97.0%). Conclusions: The nomogram provided a noninvasive and effective means of assessing cardiac involvement in systemic amyloidosis, offering a valuable aid for clinical decision‐making and patient management.
      pubtype: Academic Journal
      doctype:
        diagnostic images
        research
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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