Design, implementation and evaluation of a model of care for patients with germline predisposition to haematological malignancy and bone marrow failure syndromes.

Background: The bone marrow failure syndromes (BMFS) are clinically heterogeneous conditions with both inherited and acquired etiologies. Optimal care is often challenged by the complexity of these disorders and gaps in healthcare delivery. The Evaluating Multidisciplinary Bone maRrow fAilure CarE (...

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Publicado en:Internal Medicine Journal Vol. 55; no. 8; pp. 1350 - 1360
Autores principales: Fox, Lucy C., Goode, Erin, Den Elzen, Nicole, Cheng, Lin, Barth, Laura, Man, Kelsey, Jarmolowicz, Anna, Panjari, Mary, Best, Stephanie, Thursky, Karin, James, Paul, Bajel, Ashish, Ritchie, David, Blombery, Piers
Formato: research tables/charts Journal Article
Publicado: Wiley-Blackwell Aug2025
Acceso en línea:Ver este registro en EBSCOhost
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      dt: Aug2025
      vid: 55
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      pub: Wiley-Blackwell
      place: Malden, Massachusetts
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        188366123
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        188366123
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        10.1111/imj.70125
        188366123
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        atl: Design, implementation and evaluation of a model of care for patients with germline predisposition to haematological malignancy and bone marrow failure syndromes.
      aug:
        au:
          Fox, Lucy C.
          Goode, Erin
          Den Elzen, Nicole
          Cheng, Lin
          Barth, Laura
          Man, Kelsey
          Jarmolowicz, Anna
          Panjari, Mary
          Best, Stephanie
          Thursky, Karin
          James, Paul
          Bajel, Ashish
          Ritchie, David
          Blombery, Piers
        affil: Clinical Haematology, Peter MacCallum Cancer Centre and Royal Melbourne Hospitals, Melbourne Victoria,, Australia
      sug:
        subj:
          Hematologic Neoplasms Familial and Genetic
          Bone Marrow Diseases Familial and Genetic
          Bone Marrow Diseases Diagnosis
          Bone Marrow Diseases Therapy
          Hematologic Neoplasms Therapy
          Hematologic Neoplasms Diagnosis
          Disease Susceptibility Risk Factors
          Genetic Screening
          Mutation
          Models, Theoretical Evaluation
          Health Care Delivery
          Implementation Science
          Human
          Anemia, Hemolytic
          Health Services Accessibility
          Semi-Structured Interview
          Surveys
          Thematic Analysis
          Practice Guidelines
          Guideline Adherence
          Victoria
          Qualitative Studies
          Purposive Sample
          Data Analysis Software
      ab: Background: The bone marrow failure syndromes (BMFS) are clinically heterogeneous conditions with both inherited and acquired etiologies. Optimal care is often challenged by the complexity of these disorders and gaps in healthcare delivery. The Evaluating Multidisciplinary Bone maRrow fAilure CarE (EMBRACE) study is a multi‐stage hybrid implementation‐effectiveness study designed to explore the nature of issues faced by patients with BMFS and their physicians, and to develop, implement, and evaluate a comprehensive model of care. Methods: To identify barriers to optimal BMFS care, we conducted semi‐structured interviews with patients and patient advocates, followed by a nationwide survey of physicians involved in BMFS management. Thematic analysis was performed on interview data, and survey responses were analysed to identify common challenges and areas for improvement. Results: Interview themes elicited included: (i) limited disease‐specific awareness and resources, (ii) challenges in attaining genetic care, (iii) the ongoing impact of complex care needs, (iv) the perceived value of genetic testing, and (v) the importance of specialised healthcare professionals. Physician surveys indicated a desire for affordable genomic testing, assistance with result interpretation and genetic counselling/cascade testing of extended kindred, a forum for complex case discussion and advice regarding management strategies. Responses from patients, advocates and physicians, along with existing best‐practice guidelines, were then used to develop a 10‐component model of care aimed at addressing identified issues. Conclusions: The EMBRACE study has established a stakeholder‐informed, multidisciplinary care framework for patients with BMFS. This care programme continues to undergo evaluation and audit consistent with principles of an implementation‐effectiveness study to determine both patient and physician satisfaction, and iterative refinement to provide optimum care.
      pubtype: Academic Journal
      doctype:
        research
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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