Respiratory aspects of granulomatosis with polyangiitis (GPA).
This paper considers respiratory aspects of granulomatosis with polyangiitis (GPA), an anti-neutrophil cytoplasmic antibody (ANCA)-associated small-vessel vasculitis (AAV) formerly known as Wegener's granulomatosis. Approximately 9 out of 10 persons with GPA have some type of pulmonary or respirator...
| Publicado en: | International Journal of Child & Adolescent Health Vol. 18; no. 1; pp. 43 - 54 |
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| Autores principales: | , , , |
| Formato: | tables/charts Journal Article |
| Publicado: |
Nova Science Publishers, Inc.
2025
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| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=191503140&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 191503140 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 19395930 903I jtl: International Journal of Child & Adolescent Health issn: 19395930 maglogo: N pubinfo: dt: 2025 vid: 18 iid: 1 pid: 1040 pub: Nova Science Publishers, Inc. place: Hauppauge, New York artinfo: ui: 191503140 191503140 191503140 191503140 ppf: 43 ppct: 11 formats: fmt: @attributes: type: P tig: atl: Respiratory aspects of granulomatosis with polyangiitis (GPA). aug: au: Greydanus, Donald E. Bhave, Swati Y. Ashok, Narmada Goel, Ashish affil: Department of Pediatric and Adolescent Medicine, Western Michigan University Homer Stryker MD School of Medicine, Kalamazoo, Michigan, USA sug: subj: Granulomatosis with Polyangiitis Antibodies, Antineutrophil Cytoplasmic Vasculitis Granulomatosis with Polyangiitis Epidemiology Granulomatosis with Polyangiitis Etiology Granulomatosis with Polyangiitis Symptoms Granulomatosis with Polyangiitis Diagnosis Granulomatosis with Polyangiitis Prevention and Control Granulomatosis with Polyangiitis Therapy Radiography, Thoracic Tomography, X-Ray Computed Magnetic Resonance Imaging Bronchoalveolar Lavage Bronchoscopy Biopsy Respiratory Tract Diseases ab: This paper considers respiratory aspects of granulomatosis with polyangiitis (GPA), an anti-neutrophil cytoplasmic antibody (ANCA)-associated small-vessel vasculitis (AAV) formerly known as Wegener's granulomatosis. Approximately 9 out of 10 persons with GPA have some type of pulmonary or respiratory disease that may include upper or lower respiratory tract features. Upper respiratory tract issues include otitis, hearing impairment, oral/nasal ulcers, rhinitis, sinusitis, saddle-nose deformity and/or subglottic stenosis. Lower respiratory tract issues include hemoptysis, pulmonary hemorrhage, pleurisy, pulmonary nodules and/or pulmonary infiltrates. Topics considered include concepts of epidemiology, clinical features, diagnostic evaluation and management of pulmonary aspects of GPA. A challenging aspect of this condition is the overlapping aspects with other small vessel vasculitides. pubtype: Academic Journal doctype: tables/charts Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
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