Long‐term remission with ustekinumab in a patient with pyogenic arthritis, pyoderma gangrenosum and acne (PAPA) syndrome suggests the importance of interleukin‐12/interleukin‐23 cytokines in PSTPIP1–associated inflammatory diseases

This article focuses on the clinical presentation and treatment response of a family affected by proline/serine/threonine phosphatase–interacting protein 1 (PSTPIP1)–associated inflammatory disease, specifically pyogenic arthritis, pyoderma gangrenosum, and acne (PAPA) syndrome. The mother, carrying...

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Detalles Bibliográficos
Publicado en:Arthritis & Rheumatology Vol. 78; no. 4; pp. 1000 - 1005
Autores principales: Wittmann, Nico, Nell, Dominik, Mohs, Magdalena, Grude, Marie C., Mishra, Neha, Meyer‐Bahlburg, Almut, Bossaller, Lukas
Formato: case study letter pictorial tables/charts Journal Article
Publicado: Wiley-Blackwell Apr2026
Acceso en línea:Ver este registro en EBSCOhost