Occupational therapy intervention in a child with multicentric carpotarsal osteolysis: Case report.

Introduction: Multicentric Carpotarsal Osteolysis (MCTO) is a rare, genetic disabling disease beginning in early childhood, resulting in the destruction and resorption of carpal and tarsal bones. The aim of this study was to describe the occupational therapy intervention on a child with MCTO to eval...

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Publicado en:British Journal of Occupational Therapy Vol. 89; no. 6; pp. 396 - 404
Autores principales: Marina, Usai, Marianna, Gaito, Chiara, Tacchino, Anna Bruna, Ronchetti, Silvia, Semino, Ludovica, Primavera, Maja, Di Rocco, Paolo, Moretti, Simeon, Rachele, Marta, Bertamino
Formato: case study pictorial tables/charts Journal Article
Publicado: Sage Publications Inc. Jun2026
Acceso en línea:Ver este registro en EBSCOhost
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      dt: Jun2026
      vid: 89
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      pub: Sage Publications Inc.
      place: Thousand Oaks, California
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        atl: Occupational therapy intervention in a child with multicentric carpotarsal osteolysis: Case report.
      aug:
        au:
          Marina, Usai
          Marianna, Gaito
          Chiara, Tacchino
          Anna Bruna, Ronchetti
          Silvia, Semino
          Ludovica, Primavera
          Maja, Di Rocco
          Paolo, Moretti
          Simeon, Rachele
          Marta, Bertamino
        affil: Physical Medicine and Rehabilitation Unit, IRCCS Istituto Giannina Gaslini, Genoa, Italy
      sug:
        subj:
          Occupational Therapy
          Osteolysis Rehabilitation
          Abnormalities, Multiple Rehabilitation
          Male
          Child, Preschool
          Activities of Daily Living Evaluation
          Patient Autonomy Evaluation
          Mutation
          Tarsal Joint Pathology
          Kidney Failure, Chronic
          Walkers
          International Classification of Functioning, Disability, and Health
          Multidisciplinary Care Team
          Social Participation Evaluation
          Wheelchairs
          Caregivers Education
          Task Performance and Analysis
          Adaptation, Psychological
          Treatment Outcomes
          Personal Satisfaction
          Chronic Pain
          Hyperopia
          Physical Examination
          Clinical Assessment Tools
          After Care
          Physical Therapy
          Activities of Daily Living
          Patient Participation
          Needs Assessment
          Physical Mobility
          Functional Assessment
          Equipment Design
          Play and Playthings
          Social Participation
          Self Care
          Assistive Technology Devices
          Family Role
          Child, Preschool: 2-5 years
          Male
      ab: Introduction: Multicentric Carpotarsal Osteolysis (MCTO) is a rare, genetic disabling disease beginning in early childhood, resulting in the destruction and resorption of carpal and tarsal bones. The aim of this study was to describe the occupational therapy intervention on a child with MCTO to evaluate the impact of the treatment on daily function, autonomy, and participation in activities of daily living. Methods and case description: Interventions focused on self-care, power wheelchair mobility, and environmental adaptations. The Canadian Occupational Performance Measure measured the child's progress. After 5 months, he was independent in directing his care and driving his power wheelchair; he also increased participation in games and social activities with peers. Conclusions: The intervention process and the occupational therapist's role are detailed. This study contributes to future research to create standards of care aimed at improving patients' functional independence and quality of life.
      pubtype: Academic Journal
      doctype:
        case study
        pictorial
        tables/charts
        Journal Article
      ougenre: Article
    language: English
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