Pioderma gangrenoso-like genital: inicio de la enfermedad de Behçet.

BACKGROUND: Behçet’s syndrome is a chronic inflammatory disease of variable course characterized by multiorgan involvement with phases of remission. Its most frequent clinical manifestations are mucocutaneous, given by the genital and oral ulcers. CLINICAL CASE: A 20-year-old female patient who had...

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Publicado en:Dermatología Revista Mexicana Vol. 70; no. 2; pp. 280 - 286
Autores principales: Jiménez Segura, Ana María, Ochoa Bermúdez, Juan Felipe, Ojeda Trujillo, Carlos Alberto, Saavedra, Adriana
Formato: Artículo
Publicado: Edicion y Farmacia S.A. de C.V. mar/abr2026
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Acceso en línea:Ver este registro en EBSCOhost
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        atl: Pioderma gangrenoso-like genital: inicio de la enfermedad de Behçet.
      aug:
        au:
          Jiménez Segura, Ana María
          Ochoa Bermúdez, Juan Felipe
          Ojeda Trujillo, Carlos Alberto
          Saavedra, Adriana
        affil:
          Residente de dermatología, Fundación Universitaria Sanitas.
          Universidad Nacional de Colombia, Bogotá, Colombia.
          Universidad Militar Nueva Granada, Bogotá, Colombia.
      su:
        Behçet's disease
        Pyoderma gangrenosum
        Ulcers
        Inflammation
        Differential diagnosis
        Cutaneous manifestations of general diseases
        Skin ulcers
      sug:
        subj:
          Behçet's disease
          Pyoderma gangrenosum
          Ulcers
          Inflammation
          Differential diagnosis
          Cutaneous manifestations of general diseases
          Skin ulcers
      keyword:
        Behçet syndrome
        Genital ulcers
        úlceras genitales
        pioderma gangrenoso
        Síndrome de Behçet
      ab:
        BACKGROUND: Behçet’s syndrome is a chronic inflammatory disease of variable course characterized by multiorgan involvement with phases of remission. Its most frequent clinical manifestations are mucocutaneous, given by the genital and oral ulcers. CLINICAL CASE: A 20-year-old female patient who had an extensive, painful, and destructive vaginal ulcer, pyoderma gangrenosum type, as the first manifestation of Behçet’s syndrome. CONCLUSIONS: To establish the diagnosis of Behçet’s syndrome, all the diseases encompassing the genital ulcerative syndrome must be considered, as it is a wide spectrum of differentials it becomes a diagnostic challenge when evaluating the patient.
        ANTECEDENTES: El síndrome de Behçet es un cuadro inflamatorio crónico, con un curso variable, que se caracteriza por afectación multiorgánica con etapas de remisión. Sus manifestaciones clínicas más frecuentes son las mucocutáneas, sobre todo úlceras genitales y orales. CASO CLÍNICO: Paciente femenina de 20 años que inició su padecimiento con una úlcera vaginal extensa, dolorosa, destructiva (pioderma gangrenoso-like) como primera manifestación del síndrome de Behçet. CONCLUSIONES: Para establecer el diagnóstico de síndrome de Behçet deben tenerse en cuenta todas las enfermedades que engloban el síndrome de úlceras genitales; debido al amplio espectro de diagnósticos diferenciales, el síndrome de Behçet es un reto diagnóstico al momento de evaluar al paciente.
      pubtype: Academic Journal
      doctype: Article
      src: R
    language: Spanish
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