Degeneración marginal pelúcida y úlcera corneal asociadas a síndrome de Sjögren.

Clinical cases: two cases reported presented corneal topography with peripheral inferior corneal slimming (pachymetry), flattening of superior and central meridian, high stigmatism against the rule, corroborating clinical pellucid marginal degeneration prognosis. A rheumatologist and a dermatologist...

Descripción completa

Detalles Bibliográficos
Publicado en:Revista Medica del IMSS Vol. 47; no. 1; pp. 77 - 83
Autores principales: Fernández-Barboza, Fernando, Verdiguel-Sotelo, Karla, Hernández-López, Adriana
Formato: Artículo
Publicado: Direccion de Prestaciones Medicas - IMSS ene/feb2009
Materias:
Acceso en línea:Ver este registro en EBSCOhost
fields @attributes:
  recordID: 1
pdfLink:
plink: https://search.ebscohost.com/login.aspx?direct=true&db=lth&AN=37039616&site=ehost-live
header:
  @attributes:
    shortDbName: lth
    uiTerm: 37039616
    longDbName: MedicLatina
    uiTag: AN
  controlInfo:
    bkinfo:
    jinfo:
      jid:
        04435117
        7L1
      jtl: Revista Medica del IMSS
      issn: 04435117
      maglogo: N
    pubinfo:
      dt: ene/feb2009
      vid: 47
      iid: 1
      pid: 20867
      pub: Direccion de Prestaciones Medicas - IMSS
    artinfo:
      ui: 37039616
      ppf: 77
      ppct: 6
      formats:
        fmt:
          @attributes:
            type: P
            size: 266KB
      tig:
        atl: Degeneración marginal pelúcida y úlcera corneal asociadas a síndrome de Sjögren.
      aug:
        au:
          Fernández-Barboza, Fernando
          Verdiguel-Sotelo, Karla
          Hernández-López, Adriana
        affil: Hospital de Especialidades, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, Distrito Federal, México
      su:
        Corneal topography
        Rheumatologists
        Astigmatism
        Visual acuity
        Dry eye syndromes
      sug:
        subj:
          Corneal topography
          Rheumatologists
          Astigmatism
          Visual acuity
          Dry eye syndromes
      keyword:
        astigmatism
        corneal diseases
        corneal topography
        corneal ulcer
        Sjogren's syndrome
        úlcera de la córnea
        astigmatismo
        enfermedades de la córnea
        síndrome de Sjögren
        topografía de la córnea
      ab:
        Clinical cases: two cases reported presented corneal topography with peripheral inferior corneal slimming (pachymetry), flattening of superior and central meridian, high stigmatism against the rule, corroborating clinical pellucid marginal degeneration prognosis. A rheumatologist and a dermatologist confirmed primary and secondary Sjögren in each case. Conclusions: In the cases studied, the pellucid marginal degeneration was presented with inferior corneal slimming, progressive irregular astigmatism and decreased visual acuity. However, the patients were treated for a long time only for dry eye. The association between pellucid marginal degeneration, primary Sjögren syndrome and secondary Sjögren syndrome has not been described. In the analyzed cases, both pathologies were observed and caused a bad prognosis because the treatment required is very difficult.
        Casos clínicos: en dos pacientes se observó topografía corneal con adelgazamiento inferior periférico (paquimetría), aplanamiento superior y meridiano central, astigmatismo elevado en contra de la regla; se corroboró sospecha clínica de degeneración marginal pelúcida. En los servicios de reumatología y dermatología se diagnosticó síndrome de Sjögren primario y secundario. Conclusiones: la degeneración marginal pelúcida se presentó con adelgazamiento corneal inferior, astigmatismo irregular progresivo con disminución de la agudeza visual, sin embargo, las pacientes fueron tratadas durante mucho tiempo solo por síndrome de ojo seco. No se ha descrito la asociación entre degeneración marginal pelúcida y síndrome de Sjögren primario y secundario. En los casos estudiados se presentaron ambas patologías a la vez, empeorando el pronóstico por las complicaciones y las dificultades en el tratamiento.
      pubtype: Academic Journal
      doctype: Article
      src: R
    language: Spanish
    refInfo:
    copyright:
      @attributes:
        flag: Y
      custom: Copyright of Revista Medica del IMSS is the property of Direccion de Prestaciones Medicas - IMSS and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use.
      item: Revista Medica del IMSS
      holder: Direccion de Prestaciones Medicas - IMSS
      dt:
        @attributes:
          year: 2009
    holdings:
      @attributes:
        islocal: N