Fast Facts: Long-Chain Fatty Acid Oxidation Disorders [Japanese]

Disorders affecting the oxidation of long-chain fatty acids are complex, potentially life-threatening, metabolic conditions. A number of genetically distinct conditions exist, depending on the gene and protein affected, but there are some common clinical and biochemical features. Newborn screening,...

Descripción completa

Detalles Bibliográficos
Autores principales: Barbara K., Burton, Anne, Daly
Formato: Libro
Publicado: S. Karger 2025
Materias:
Acceso en línea:Ver este registro en EBSCOhost
fields @attributes:
  recordID: 1
pdfLink:
plink: https://search.ebscohost.com/login.aspx?direct=true&db=nlebk&AN=4355897&site=ehost-live
header:
  @attributes:
    shortDbName: nlebk
    uiTerm: 4355897
    longDbName: eBook Collection (EBSCOhost)
    uiTag: AN
  controlInfo:
    bkinfo:
      btl: Fast Facts: Long-Chain Fatty Acid Oxidation Disorders [Japanese]
      aug:
        au:
          Barbara K., Burton
          Anne, Daly
      isbn:
        9783318073768
        9783318074987
        9783318074994
    imageinfo:
    pubinfo:
      dt:
        @attributes:
          year: 2025
          month: 01
          day: 01
      dtAvail:
        @attributes:
          year: 2026
          month: 02
          day: 11
      ed: 1st
      pub: S. Karger
      pubContract: Karger AG (Open Access)
      place: Basel
      price: 0.01
      limitsGroup:
        maxCheckoutDays: 1500
        pda: N
        printPagesOffline: 100
        printPagesOnline: 100
        previewPages: 10000
      prePubGroup:
        dewey:
          @attributes:
            class: 618.9239
            item: 618 .9239
        lc:
          @attributes:
            class: RJ390
            item: RJ 390
    artinfo:
      ui:
        4355897
        1550575974
      formats:
        fmt:
          – @attributes:
              type: EB
              doid: NL$4355897$PDF
              caption: PDF
              download: Y
          – @attributes:
              type: EK
              doid: NL$4355897$EPUB
              caption: EPUB
              download: Y
      tig:
        atl: Fast Facts: Long-Chain Fatty Acid Oxidation Disorders [Japanese]
        ptl: Fast Facts
      aug:
        au:
          Barbara K., Burton
          Anne, Daly
      su:
        Fatty acids
        Metabolic disorders in children
      sug:
        subj:
          MEDICAL / Endocrinology & Metabolism
          Fatty acids
          Metabolic disorders in children
      ab: Disorders affecting the oxidation of long-chain fatty acids are complex, potentially life-threatening, metabolic conditions. A number of genetically distinct conditions exist, depending on the gene and protein affected, but there are some common clinical and biochemical features. Newborn screening, which allows early intervention to prevent long-term morbidity, is not universally available. Even with screening, it is important that health professionals recognize the symptoms that may manifest at different stages of life. This concise guide to these rare conditions will be of value to all health professionals who may encounter or care for an individual with a long-chain fatty acid oxidation disorder. As well as explaining the underlying defects, inheritance and how the conditions manifest, the book describes the diagnosis and differential diagnosis of the disorders. The final chapter gives some guidance on genetic counseling and supporting patients.
      pubtype: eBook
      doctype: Book
      ougenre: Book
    language: Japanese
    copyright:
      @attributes:
        flag: N
      copyrightText:
    holdings:
      @attributes:
        islocal: N