Dermatosis paraneoplásicas. Revisión de la bibliografía.

The paraneoplasic dermatosis represent a heterogeneous group of clinical manifestations that appear as an expression of the action at a distance which can exercise a neoplasm. They constitute the second paraneoplasic syndrome in frequency, being surpassed only by the endocrine paraneoplásicas entiti...

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Detalles Bibliográficos
Publicado en:Medicina Interna de México Vol. 27; no. 6; pp. 586 - 596
Autores principales: Rivera Martínez, Arturo A., López Hernández, Marco A.
Formato: Artículo
Publicado: Colegio de Medicina Interna de Mexico nov/dic2011
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Acceso en línea:Ver este registro en EBSCOhost
Descripción
Sumario:The paraneoplasic dermatosis represent a heterogeneous group of clinical manifestations that appear as an expression of the action at a distance which can exercise a neoplasm. They constitute the second paraneoplasic syndrome in frequency, being surpassed only by the endocrine paraneoplásicas entities. There are several ways to classify them, which is discussed in this review article; paraneoplasic dermatosis cover a wide variety of manifestations, here will be revised: acanthosis nigricans, adquired ichthyosis, Bazex syndrome, paraneoplastic pemphigus, Leser-Trelat syndrome, Erythema gyratum repens, Sweet syndrome, dermatomyositis, migratory erythema syndrome, pyoderma gangrenosum, juvenile necrobiotic xanthogranuloma and the acquired hypertrichosis. The paraneoplasic dermatosis are rare dermatological entities, of difficult recognition, which may pass unnoticed to be as mild and little annoying problems which makes that the patient's own paid them little attention. Recognize the characteristics of the paraneoplasic dermatosis injuries facilitates the early detection of hidden cancer whose own demonstrations, would probably appear months or even years later, therefore, the finding of these dermatosis allows early suspect the tumor which are associated, thus increasing the survival of patients. In many cases can not explain the pathogenesis of the Association, but found that the treatment of the underlying neoplasm will lead to the cure of the dermatosis.
Las dermatosis paraneoplásicas son un grupo heterogéneo de manifestaciones clínicas que aparecen como expresión de las acciones a distancia que puede ejercer una neoplasia. Constituyen el segundo síndrome paraneoplásico en frecuencia, sólo superado por las enfermedades paraneoplásicas endocrinológicas. Reconocer las lesiones características de la dermatosis paraneoplásica facilita la identificación temprana de un cáncer oculto cuyas manifestaciones propias quizá aparezcan meses o años después. Por esto, el hallazgo de estas dermatosis permite sospechar tempranamente el tumor con el que se asocian, incrementando así la supervivencia de los pacientes. En muchos casos no puede precisarse la etiopatogenia de la asociación, pero se ha comprobado que el tratamiento de la neoplasia subyacente llevará a la cura de la dermatosis.