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Dental Findings and Management in a Mucopolysaccharidosis Type IIIB Patient.

Mucopolysaccharidosis type IIIB (MPS IIIB) is an autosomal recessive disorder caused by deficiency of the lysosomal enzyme a-N-acetylglucosaminidase. Affected subjects present developmental delay, attention deficit disorder, uncontrollable hyperactivity, and aggressive behavior, followed by progress...

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Published in:Journal of Dentistry for Children Vol. 79; no. 3; pp. 176 - 181
Main Authors: de Siqueira Mellara, Talitha, Torres Azevedo, Danielle, Faria, Gisele, Nelson Filho, Paulo, de Queiroz, Alexandra Mussolino, Guilherme Brentegani, Luiz
Format: case study diagnostic images pictorial Journal Article
Published: American Academy of Pediatric Dentistry Sep-Dec2012
Online Access:View this record in EBSCOhost
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      dt: Sep-Dec2012
      vid: 79
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      pub: American Academy of Pediatric Dentistry
      place: Chicago, Illinois
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        atl: Dental Findings and Management in a Mucopolysaccharidosis Type IIIB Patient.
      aug:
        au:
          de Siqueira Mellara, Talitha
          Torres Azevedo, Danielle
          Faria, Gisele
          Nelson Filho, Paulo
          de Queiroz, Alexandra Mussolino
          Guilherme Brentegani, Luiz
        affil: School of Dentistry, University of São Paulo at Ribeirão Preto, Brazil
      sug:
        subj:
          Mucopolysaccharidosis II Complications
          Dentistry, Operative
          Tooth Diseases Diagnosis
          Tooth Diseases Therapy
          Periodontal Diseases Diagnosis
          Periodontal Diseases Therapy
          Child
          Male
          Tooth Radiography
          Dental Care for Disabled
          Child: 6-12 years
          Male
      ab: Mucopolysaccharidosis type IIIB (MPS IIIB) is an autosomal recessive disorder caused by deficiency of the lysosomal enzyme a-N-acetylglucosaminidase. Affected subjects present developmental delay, attention deficit disorder, uncontrollable hyperactivity, and aggressive behavior, followed by progressive dementia and death in late adolescence. The purpose of this paper is to report the dental findings and treatment in a child with MPS IIIB. His primary molars and permanent mandibular incisors presented obliterated pulp chambers and root canals, which may be a clinical manifestation of this disorder.
      pubtype: Academic Journal
      doctype:
        case study
        diagnostic images
        pictorial
        Journal Article
      ougenre: Article
    language: English
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