Periodic Fever: A Review on Clinical, Management and Guideline for Iranian Patients - Part II.
Periodic fever syndromes are a group of diseases characterized by episodes of fever with healthy intervals between febrile episodes. In the first part of this paper, we presented a guideline for approaching patients with periodic fever and reviewed two common disorders with periodic fever in Iranian...
| Publicado en: | Iranian Journal of Pediatrics Vol. 24; no. 3; pp. 229 - 241 |
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| Autores principales: | , , , , , |
| Formato: | review tables/charts Journal Article |
| Publicado: |
Brieflands
Jun2014
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| Acceso en línea: | Ver este registro en EBSCOhost |
| fields | @attributes: recordID: 1 pdfLink: plink: https://search.ebscohost.com/login.aspx?direct=true&db=ccm&AN=96727719&site=ehost-live header: @attributes: shortDbName: ccm uiTerm: 96727719 longDbName: CINAHL Complete uiTag: AN controlInfo: bkinfo: dissinfo: jinfo: jid: 20082142 5DI1 jtl: Iranian Journal of Pediatrics issn: 20082142 maglogo: N pubinfo: dt: Jun2014 vid: 24 iid: 3 pid: 69510 pub: Brieflands place: , <Blank> artinfo: ui: 96727719 96727719 103966438 96727719 ppf: 229 ppct: 12 formats: tig: atl: Periodic Fever: A Review on Clinical, Management and Guideline for Iranian Patients - Part II. aug: au: Ahmadinejad, Zahra Mansouri, Sedigeh Ziaee, Vahid Aghighi, Yahya Moradinejad, Mohammad-Hassan Fereshteh-Mehregan, Fatemeh affil: Department of Infectious Diseases, Imam Khomeini Hospital sug: subj: Mevalonate Kinase Deficiency Diagnosis Mevalonate Kinase Deficiency Therapy Sweet's Syndrome Blau Syndrome Cryopyrin-Associated Periodic Syndromes Bone Diseases Immunoglobulins Tumor Necrosis Factor Receptor-Associated Periodic Syndrome Muckle-Wells Syndrome Practice Guidelines Iran ab: Periodic fever syndromes are a group of diseases characterized by episodes of fever with healthy intervals between febrile episodes. In the first part of this paper, we presented a guideline for approaching patients with periodic fever and reviewed two common disorders with periodic fever in Iranian patients including familial Mediterranean fever (FMF) and periodic fever syndromes except for periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA). In this part, we review other autoinflammatory disorders including hyper IgD, tumor necrosis factor receptor-associated periodic syndrome (TRAPS), cryopyrin associated periodic syndromes, autoinflammatory bone disorders and some other rare autoinflammatory disorders such as Sweet's and Blau syndromes. In cryopyrin associated periodic syndromes group, we discussed chronic infantile neurologic cutaneous and articular (CINCA) syndrome, Muckle-Wells syndrome and familial cold autoinflammatory syndrome. Autoinflammatory bone disorders are categorized to monogenic disorders such as pyogenic arthritis, pyoderma ;gangraenosum and acne (PAPA) syndrome, the deficiency of interleukine-1 receptor antagonist (DIRA) and Majeed syndrome and polygenic background or sporadic group such as chronic recurrent multifocal osteomyelitis (CRMO) or synovitis, acne, pustulosis, hyperostosis and osteitis (SAPHO) syndrome are classified in sporadic group. Other autoinflammatory syndromes are rare causes of periodic fever in Iranian system registry. pubtype: Academic Journal doctype: review tables/charts Journal Article ougenre: Article language: English refInfo: holdings: @attributes: islocal: N |
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