Paroxysmal phenomena in severe disabled children with refractory seizures. From clinical to long-video-EEG processing data to re-examine suspect events.

To provide an estimate of the occurrence of misdiagnosis in paroxysmal events in institutionalized children with severe disabilities and refractory epilepsy. A multi-step diagnostic survey, from observational to long-term video-EEG monitoring was performed in 46 severe disabled children. Multirater...

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Publicado en:Research in Developmental Disabilities Vol. 36; pp. 125 - 134
Autores principales: Arcieri, Salvatore, Zanotta, Nicoletta, Gnatkovsky, Vadym, Avantaggiato, Paolo, Formica, Francesca, Epifanio, Roberta, Angelini, Lucia, Strazzer, Sandra, Zucca, Claudio
Formato: Journal Article
Publicado: Pergamon Press - An Imprint of Elsevier Science Jan2015
Acceso en línea:Ver este registro en EBSCOhost
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        atl: Paroxysmal phenomena in severe disabled children with refractory seizures. From clinical to long-video-EEG processing data to re-examine suspect events.
      aug:
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          Arcieri, Salvatore
          Zanotta, Nicoletta
          Gnatkovsky, Vadym
          Avantaggiato, Paolo
          Formica, Francesca
          Epifanio, Roberta
          Angelini, Lucia
          Strazzer, Sandra
          Zucca, Claudio
        affil: Unit of Clinical Neurophysiology, Scientific Institute IRCCS E. Medea, Via Don Luigi Monza 20/A, 23842 Bosisio Parini, LC, Italy
      sug:
      ab: To provide an estimate of the occurrence of misdiagnosis in paroxysmal events in institutionalized children with severe disabilities and refractory epilepsy. A multi-step diagnostic survey, from observational to long-term video-EEG monitoring was performed in 46 severe disabled children. Multirater Kappa statistic was used to assess agreement between investigators and to individualize children who remained with dubious events. Subsequently, prolonged EEG-video monitoring analysis was performed in selected children to define phenomena due to seizures. A total of 128 video records were performed, 64 routine video-EEG and 27 long-monitoring video-EEG data were screened for detailed analysis. Thirty (21 female, 9 male) children (65%) with dubious seizures were identified by video records (concordance K=0.63). Of these, in 18 children (39%) seizures were excluded by routine video-EEG monitoring (K=0.86). Twelve children (26%) required accurate investigations with long-term video-EEG. In 5 children (11%), 3 symptomatic and 2 cryptogenic, very short and subtle seizures were confirmed by investigators concordance (K=0.83). Distinguishing paroxysmal phenomena is a challenge in children with severe disabilities; its most remarkable consequence is inappropriate pharmacological treatment and social costs. Our data suggest that the frequency of misdiagnosis could have been underestimated. The clinicians who manage children with severe disabilities and refractory epilepsy must remain alert to risk of an incorrect treatment.
      pubtype: Academic Journal
      doctype: Journal Article
      ougenre: Article
    language: English
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