Clear cell sarcoma expressing a novel chimerical transcript EWSR1 exon 7/ATF1 exon 6.

Clear cell sarcoma harbours recurrent translocation, resulting in EWSR1/ATF1 or less commonly EWSR1/CREB1 fusion. To date, six types of EWSR1/ATF1 fusion have been reported, of which three are in-frame and encode functional proteins. We present a reverse transcription - polymerase chain reaction ana...

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Publicado en:Virchows Archiv: European Journal of Pathology Vol. 461; no. 3; pp. 339 - 344
Autores principales: Gineikiene E, Seinin D, Brasiuniene B, Brazaitis A, Griskevicius L, Jakubauskas A, Gineikiene, Egle, Seinin, Dmitrij, Brasiuniene, Birute, Brazaitis, Andrius, Griskevicius, Laimonas, Jakubauskas, Arturas
Formato: case study Journal Article
Publicado: Springer Nature Sep2012
Acceso en línea:Ver este registro en EBSCOhost
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      jtl: Virchows Archiv: European Journal of Pathology
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      dt: Sep2012
      vid: 461
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      pub: Springer Nature
      place: New York, New York
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        10.1007/s00428-012-1295-y
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        atl: Clear cell sarcoma expressing a novel chimerical transcript EWSR1 exon 7/ATF1 exon 6.
      aug:
        au:
          Gineikiene E
          Seinin D
          Brasiuniene B
          Brazaitis A
          Griskevicius L
          Jakubauskas A
          Gineikiene, Egle
          Seinin, Dmitrij
          Brasiuniene, Birute
          Brazaitis, Andrius
          Griskevicius, Laimonas
          Jakubauskas, Arturas
        affil: Hematology, Oncology and Transfusion Medicine Center, Vilnius University Hospital Santariskiu Klinikos, Santariskiu 2, Vilnius 08661, Lithuania
      sug:
        subj:
          Proteins
          Sarcoma
          Soft Tissue Neoplasms
          Adult
          Antineoplastic Agents, Combined
          Bone Neoplasms
          Genes
          Fatal Outcome
          Toes
          Neoplasm Metastasis
          Male
          Reverse Transcriptase Polymerase Chain Reaction
          Soft Tissue Neoplasms Drug Therapy
          Soft Tissue Neoplasms Pathology
          Chromosome Disorders
          Adult: 19-44 years
          Male
      ab: Clear cell sarcoma harbours recurrent translocation, resulting in EWSR1/ATF1 or less commonly EWSR1/CREB1 fusion. To date, six types of EWSR1/ATF1 fusion have been reported, of which three are in-frame and encode functional proteins. We present a reverse transcription - polymerase chain reaction analysis of a tumour near the hallux of the right foot. The sequencing of obtained fragments revealed the presence of a novel chimerical transcript-the in-frame fusion between EWSR1 exon 7 and ATF1 exon 6 that represents the fourth in-frame type of EWSR1/ATF1 fusion identified in clear cell sarcomas.
      pubtype: Academic Journal
      doctype:
        case study
        Journal Article
      ougenre: Article
    language: English
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