Bullous Pyoderma Gangrenosum Associated with Antiphospholipid Syndrome: A Case Report and Literature Review.

We report a rare case of a middle-aged Omani woman who was known to have primary antiphospholipid syndrome, glucose-6-phosphate dehydrogenase deficiency, and iron deficiency anaemia. Cannulation attempts caused bulla which progressed to ulceration. A pathergy phenomenon with high suspicion of pyoder...

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Bibliographic Details
Published in:Oman Medical Journal Vol. 39; no. 4; pp. 14 - 20
Main Authors: Al-Bahrani, Mayar, Alwashahi, Yousuf, Almoqbali, Ahmed, Alajmi, Asma
Format: case study pictorial Journal Article
Published: Oman Medical Specialty Board Jul2024
Online Access:View this record in EBSCOhost
Description
Summary:We report a rare case of a middle-aged Omani woman who was known to have primary antiphospholipid syndrome, glucose-6-phosphate dehydrogenase deficiency, and iron deficiency anaemia. Cannulation attempts caused bulla which progressed to ulceration. A pathergy phenomenon with high suspicion of pyoderma gangrenosum was postulated. Management with corticosteroids, cyclosporin, and finally ustekinumab, a novel biologic agent, yielded a beneficial response.