Genotype, phenotype, and clinical course in five patients with PAPA syndrome (pyogenic sterile arthritis, pyoderma gangrenosum, and acne).

Objective To describe the genotypes, phenotypes, immunophenotypes, and treatments of PAPA syndrome (pyogenic sterile arthritis, pyoderma gangrenosum, and acne), a rare autoinflammatory disease, in 5 patients. Methods Clinical information was gathered from medical records and through interviews with...

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Bibliographic Details
Published in:Arthritis & Rheumatism Vol. 64; no. 6; pp. 2022 - 2028
Main Authors: Demidowich, Andrew P., Freeman, Alexandra F., Kuhns, Douglas B., Aksentijevich, Ivona, Gallin, John I., Turner, Maria L., Kastner, Daniel L., Holland, Steven M.
Format: pictorial research tables/charts Journal Article
Published: Wiley-Blackwell Jun2012
Online Access:View this record in EBSCOhost