Pyoderma gangrenosum as a cause of splenomegaly and association with a T-cell clone.

The spectrum of clinical presentation of haematological disease is wide. We highlight two features of this principle: a rare cause of a ‘haematological’ presentation and a possible haematological cause of a disease not normally considered as such. A case of systemic pyoderma gangrenosum presented wi...

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Bibliographic Details
Published in:Clinical & Laboratory Haematology Vol. 27; no. 6; pp. 402 - 405
Main Authors: Mittal S, Milner BJ, Vickers MA
Format: case study tracings Journal Article
Published: Wiley-Blackwell Dec2005
Online Access:View this record in EBSCOhost
Description
Summary:The spectrum of clinical presentation of haematological disease is wide. We highlight two features of this principle: a rare cause of a ‘haematological’ presentation and a possible haematological cause of a disease not normally considered as such. A case of systemic pyoderma gangrenosum presented with splenomegaly in the absence of a rash. A clonal γ- and β-T-cell receptor rearrangement was demonstrated. Such clones may be a general phenomenon involved in the pathogenesis of this condition.